PAX6
paired box 6 | AN, D11S812E, WAGR, AN1, AN2

This gene encodes paired box protein Pax-6, one of many human homologs of the Drosophila melanogaster gene prd. In addition to a conserved paired box domain, a hallmark feature of this gene family, the encoded protein also contains a homeobox domain. Both domains are known to bind DNA and function as regulators of gene transcription. Activity of this protein is key in the development of neural tissues, particularly the eye. This gene is regulated by multiple enhancers located up to hundreds of kilobases distant from this locus. Mutations in this gene or in the enhancer regions can cause ocular disorders such as aniridia and Peter's anomaly. Use of alternate promoters and alternative splicing results in multiple transcript variants encoding different isoforms. Interestingly, inclusion of a particular alternate coding exon has been shown to increase the length of the paired box domain and alter its DNA binding specificity. Consequently, isoforms that carry the shorter paired box domain regulate a different set of genes compared to the isoforms carrying the longer paired box domain. [provided by RefSeq, Mar 2019]

Member of: DE-4 DE-4.28 Developmental clusters: GC7
Biological processes 84 terms
DNA binding (GO:0003677)DNA binding (GO:0003677)DNA-binding transcription activator activity, RNA polymerase II-specific (GO:0001228)DNA-binding transcription activator activity, RNA polymerase II-specific (GO:0001228)DNA-binding transcription factor activity (GO:0003700)DNA-binding transcription factor activity (GO:0003700)DNA-binding transcription factor activity, RNA polymerase II-specific (GO:0000981)DNA-binding transcription factor activity, RNA polymerase II-specific (GO:0000981)DNA-binding transcription factor activity, RNA polymerase II-specific (GO:0000981)DNA-binding transcription factor activity, RNA polymerase II-specific (GO:0000981)DNA-binding transcription repressor activity, RNA polymerase II-specific (GO:0001227)HMG box domain binding (GO:0071837)R-SMAD binding (GO:0070412)R-SMAD binding (GO:0070412)RNA binding (GO:0003723)RNA polymerase II cis-regulatory region sequence-specific DNA binding (GO:0000978)RNA polymerase II cis-regulatory region sequence-specific DNA binding (GO:0000978)RNA polymerase II cis-regulatory region sequence-specific DNA binding (GO:0000978)RNA polymerase II core promoter sequence-specific DNA binding (GO:0000979)anatomical structure morphogenesis (GO:0009653)animal organ morphogenesis (GO:0009887)blood vessel development (GO:0001568)brain development (GO:0007420)camera-type eye development (GO:0043010)central nervous system development (GO:0007417)central nervous system development (GO:0007417)cerebral cortex development (GO:0021987)chromatin (GO:0000785)chromatin (GO:0000785)chromatin (GO:0000785)chromatin DNA binding (GO:0031490)chromatin binding (GO:0003682)chromatin remodeling (GO:0006338)co-SMAD binding (GO:0070410)cornea development in camera-type eye (GO:0061303)cytoplasm (GO:0005737)eye development (GO:0001654)forebrain development (GO:0030900)glucose homeostasis (GO:0042593)histone acetyltransferase binding (GO:0035035)histone acetyltransferase binding (GO:0035035)iris morphogenesis (GO:0061072)negative regulation of neurogenesis (GO:0050768)negative regulation of transcription by RNA polymerase II (GO:0000122)negative regulation of transcription by RNA polymerase II (GO:0000122)nervous system development (GO:0007399)nervous system development (GO:0007399)nervous system process (GO:0050877)neuron differentiation (GO:0030182)neuron fate commitment (GO:0048663)nucleoplasm (GO:0005654)nucleus (GO:0005634)nucleus (GO:0005634)nucleus (GO:0005634)pancreatic A cell development (GO:0003322)pancreatic A cell development (GO:0003322)positive regulation of DNA-templated transcription (GO:0045893)positive regulation of DNA-templated transcription (GO:0045893)positive regulation of DNA-templated transcription (GO:0045893)positive regulation of gene expression (GO:0010628)positive regulation of gene expression (GO:0010628)positive regulation of miRNA transcription (GO:1902895)positive regulation of transcription by RNA polymerase II (GO:0045944)positive regulation of transcription by RNA polymerase II (GO:0045944)positive regulation of transcription by RNA polymerase II (GO:0045944)protein binding (GO:0005515)protein kinase binding (GO:0019901)protein kinase binding (GO:0019901)regulation of DNA-templated transcription (GO:0006355)regulation of transcription by RNA polymerase II (GO:0006357)response to wounding (GO:0009611)retina development in camera-type eye (GO:0060041)sensory organ development (GO:0007423)sequence-specific DNA binding (GO:0043565)sequence-specific double-stranded DNA binding (GO:1990837)transcription cis-regulatory region binding (GO:0000976)transcription cis-regulatory region binding (GO:0000976)transcription coregulator binding (GO:0001221)transcription coregulator binding (GO:0001221)type B pancreatic cell differentiation (GO:0003309)ubiquitin protein ligase binding (GO:0031625)ventral spinal cord development (GO:0021517)ventral spinal cord development (GO:0021517)visual perception (GO:0007601)
Expression (TPM)
PAX6 — as a Regulated Gene

TFs regulating PAX6 0 TFs

Transcription factors with Perturb-seq knockdown data for PAX6. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = PAX6 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to PAX6

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of PAX6, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr11:31,797,814–31,799,520 5.9 kb Proximal (<10kb) 221
chr11:31,799,658–31,800,256 5.2 kb Proximal (<10kb) 54
chr11:31,802,527–31,803,248 2.2 kb Proximal (<10kb) 61
chr11:31,803,398–31,803,696 1.8 kb Proximal (<10kb) 41
chr11:31,804,516–31,806,498 at TSS At TSS 220
chr11:31,807,374–31,808,054 1.9 kb Proximal (<10kb) 35
chr11:31,809,858–31,815,212 4.4 kb Proximal (<10kb) 719
chr11:31,815,345–31,815,712 9.9 kb Proximal (<10kb) 78
chr11:31,815,841–31,816,162 8.2 kb Proximal (<10kb) 176
chr11:31,816,322–31,818,635 8.7 kb Proximal (<10kb) 399
chr11:31,818,793–31,819,408 7.5 kb Proximal (<10kb) 43
chr11:31,819,537–31,820,941 8.2 kb Proximal (<10kb) 197
chr11:31,822,793–31,823,338 7.8 kb Proximal (<10kb) 55
chr11:31,823,464–31,824,163 8.5 kb Proximal (<10kb) 97
chr11:31,824,867–31,825,385 9.9 kb Proximal (<10kb) 49
chr11:31,825,773–31,826,408 7.8 kb Proximal (<10kb) 114
chr11:31,826,787–31,827,506 8.8 kb Proximal (<10kb) 133

Genome Browser

Genomic view of the PAX6 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr11:31,787,814 – 31,837,506
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq