SNRNP200
small nuclear ribonucleoprotein U5 subunit 200 | Brr2, HELIC2, KIAA0788, U5-200KD, ASCC3L1, RP33

Pre-mRNA splicing is catalyzed by the spliceosome, a complex of specialized RNA and protein subunits that removes introns from a transcribed pre-mRNA segment. The spliceosome consists of small nuclear RNA proteins (snRNPs) U1, U2, U4, U5 and U6, together with approximately 80 conserved proteins. U5 snRNP contains nine specific proteins. This gene encodes one of the U5 snRNP-specific proteins. This protein belongs to the DEXH-box family of putative RNA helicases. It is a core component of U4/U6-U5 snRNPs and appears to catalyze an ATP-dependent unwinding of U4/U6 RNA duplices. Mutations in this gene cause autosomal-dominant retinitis pigmentosa. Alternatively spliced transcript variants encoding different isoforms have been found, but the full-length nature of these variants has not been determined. [provided by RefSeq, Mar 2010]

Member of: DE-11 DE-11.4 Developmental clusters: GC2
Biological processes 40 terms
ATP binding (GO:0005524)ATP hydrolysis activity (GO:0016887)RNA binding (GO:0003723)RNA binding (GO:0003723)RNA helicase activity (GO:0003724)RNA helicase activity (GO:0003724)RNA helicase activity (GO:0003724)RNA helicase activity (GO:0003724)U2-type catalytic step 1 spliceosome (GO:0071006)U2-type precatalytic spliceosome (GO:0071005)U4/U6 x U5 tri-snRNP complex (GO:0046540)U5 snRNP (GO:0005682)catalytic step 2 spliceosome (GO:0071013)cis assembly of pre-catalytic spliceosome (GO:0000354)helicase activity (GO:0004386)helicase activity (GO:0004386)identical protein binding (GO:0042802)mRNA splicing, via spliceosome (GO:0000398)mRNA splicing, via spliceosome (GO:0000398)mRNA splicing, via spliceosome (GO:0000398)mRNA splicing, via spliceosome (GO:0000398)mRNA splicing, via spliceosome (GO:0000398)membrane (GO:0016020)negative regulation of mRNA splicing, via spliceosome (GO:0048025)nucleic acid binding (GO:0003676)nucleoplasm (GO:0005654)nucleoplasm (GO:0005654)nucleus (GO:0005634)nucleus (GO:0005634)nucleus (GO:0005634)osteoblast differentiation (GO:0001649)protein binding (GO:0005515)small nuclear ribonucleoprotein complex (GO:0030532)spliceosomal complex (GO:0005681)spliceosomal complex (GO:0005681)spliceosomal snRNP assembly (GO:0000387)spliceosomal tri-snRNP complex assembly (GO:0000244)spliceosome conformational change to release U4 (or U4atac) and U1 (or U11) (GO:0000388)spliceosome conformational change to release U4 (or U4atac) and U1 (or U11) (GO:0000388)spliceosome conformational change to release U4 (or U4atac) and U1 (or U11) (GO:0000388)
Expression (TPM)
SNRNP200 — as a Regulated Gene

TFs regulating SNRNP200 0 TFs

Transcription factors with Perturb-seq knockdown data for SNRNP200. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = SNRNP200 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to SNRNP200

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of SNRNP200, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr2:96,116,133–96,117,547 188.7 kb Distal (>10kb) Multiome 470
chr2:96,138,522–96,139,006 166.8 kb Distal (>10kb) Multiome 255
chr2:96,144,225–96,145,701 160.3 kb Distal (>10kb) Multiome 423
chr2:96,148,417–96,148,969 156.8 kb Distal (>10kb) Multiome 318
chr2:96,207,850–96,209,429 96.6 kb Distal (>10kb) Multiome 1022
chr2:96,265,014–96,266,655 39.4 kb Distal (>10kb) Multiome 992
chr2:96,305,302–96,305,947 62 bp At TSS Multiome 918
chr2:96,321,245–96,322,149 16.3 kb Distal (>10kb) Multiome 640
chr2:96,325,023–96,325,881 19.8 kb Distal (>10kb) Multiome 443
chr2:96,335,437–96,336,197 30.4 kb Distal (>10kb) Multiome 847
chr2:96,507,900–96,508,563 202.6 kb Distal (>10kb) Multiome 466
chr2:96,509,253–96,509,998 204.1 kb Distal (>10kb) Multiome 525
chr2:96,531,989–96,532,491 226.7 kb Distal (>10kb) Multiome 500
chr2:96,536,180–96,538,128 231.1 kb Distal (>10kb) Multiome 684
chr2:96,538,413–96,539,012 233.2 kb Distal (>10kb) Multiome 371
chr2:96,554,285–96,554,861 249.0 kb Distal (>10kb) Multiome 435

Genome Browser

Genomic view of the SNRNP200 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr2:96,106,133 – 96,564,861
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq