CEP290
centrosomal protein 290 | 3H11Ag, BBS14, CT87, FLJ13615, JBTS5, KIAA0373, LCA10, MKS4, NPHP6, POC3, SLSN6, rd16

This gene encodes a protein with 13 putative coiled-coil domains, a region with homology to SMC chromosome segregation ATPases, six KID motifs, three tropomyosin homology domains and an ATP/GTP binding site motif A. The protein is localized to the centrosome and cilia and has sites for N-glycosylation, tyrosine sulfation, phosphorylation, N-myristoylation, and amidation. Mutations in this gene have been associated with Joubert syndrome and nephronophthisis and the presence of antibodies against this protein is associated with several forms of cancer. [provided by RefSeq, Jul 2008]

Member of: DE-2 Developmental clusters: GC2
Biological processes 43 terms
Expression (TPM)
CEP290 — as a Regulated Gene

TFs regulating CEP290 0 TFs

Transcription factors with Perturb-seq knockdown data for CEP290. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = CEP290 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to CEP290

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of CEP290, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr12:88,034,997–88,036,230 106.5 kb Distal (>10kb) Multiome 873
chr12:88,141,512–88,143,080 93 bp At TSS Multiome 892
chr12:88,143,757–88,144,303 1.9 kb Proximal (<10kb) 35
chr12:88,145,517–88,146,485 3.7 kb Proximal (<10kb) 77
chr12:88,921,388–88,922,852 780.0 kb Distal (>10kb) Multiome HiCAR 153
chr12:88,942,685–88,944,156 801.5 kb Distal (>10kb) Multiome HiCAR 122

Genome Browser

Genomic view of the CEP290 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr12:88,024,997 – 88,954,156
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq