ABCD3
ATP binding cassette subfamily D member 3 | PMP70, ZWS2, PXMP1

The protein encoded by this gene is a member of the superfamily of ATP-binding cassette (ABC) transporters. ABC proteins transport various molecules across extra- and intra-cellular membranes. ABC genes are divided into seven distinct subfamilies (ABC1, MDR/TAP, MRP, ALD, OABP, GCN20, White). This protein is a member of the ALD subfamily, which is involved in peroxisomal import of fatty acids and/or fatty acyl-CoAs in the organelle. All known peroxisomal ABC transporters are half transporters which require a partner half transporter molecule to form a functional homodimeric or heterodimeric transporter. This peroxisomal membrane protein likely plays an important role in peroxisome biogenesis. Mutations have been associated with some forms of Zellweger syndrome, a heterogeneous group of peroxisome assembly disorders. Alternative splicing results in multiple transcript variants encoding distinct isoforms. [provided by RefSeq, Jul 2008]

Member of: DE-3 DE-3.10 Developmental clusters: GC1
Biological processes 50 terms
ABC-type transporter activity (GO:0140359)ATP binding (GO:0005524)ATP binding (GO:0005524)ATP binding (GO:0005524)ATP hydrolysis activity (GO:0016887)ATP hydrolysis activity (GO:0016887)ATPase-coupled transmembrane transporter activity (GO:0042626)ATPase-coupled transmembrane transporter activity (GO:0042626)ATPase-coupled transmembrane transporter activity (GO:0042626)bile acid and bile salt transport (GO:0015721)bile acid and bile salt transport (GO:0015721)bile acid biosynthetic process (GO:0006699)bile acid biosynthetic process (GO:0006699)cytosol (GO:0005829)fatty acid beta-oxidation (GO:0006635)fatty acid beta-oxidation (GO:0006635)fatty acid beta-oxidation (GO:0006635)fatty acid biosynthetic process (GO:0006633)fatty acyl-CoA hydrolase activity (GO:0047617)identical protein binding (GO:0042802)lipid transport (GO:0006869)long-chain fatty acid import into peroxisome (GO:0015910)long-chain fatty acid import into peroxisome (GO:0015910)long-chain fatty acid import into peroxisome (GO:0015910)long-chain fatty acid transmembrane transporter activity (GO:0005324)long-chain fatty acid transmembrane transporter activity (GO:0005324)long-chain fatty acid transmembrane transporter activity (GO:0005324)membrane (GO:0016020)membrane (GO:0016020)mitochondrion (GO:0005739)peroxisomal matrix (GO:0005782)peroxisomal membrane (GO:0005778)peroxisomal membrane (GO:0005778)peroxisomal membrane (GO:0005778)peroxisomal membrane (GO:0005778)peroxisomal membrane (GO:0005778)peroxisome (GO:0005777)peroxisome (GO:0005777)peroxisome organization (GO:0007031)peroxisome organization (GO:0007031)peroxisome organization (GO:0007031)phytanic acid metabolic process (GO:1903512)phytanic acid metabolic process (GO:1903512)protein binding (GO:0005515)protein homodimerization activity (GO:0042803)response to xenobiotic stimulus (GO:0009410)transmembrane transport (GO:0055085)very long-chain fatty acid catabolic process (GO:0042760)very long-chain fatty acid catabolic process (GO:0042760)very long-chain fatty acid metabolic process (GO:0000038)
Expression (TPM)
ABCD3 — as a Regulated Gene

TFs regulating ABCD3 0 TFs

Transcription factors with Perturb-seq knockdown data for ABCD3. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = ABCD3 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to ABCD3

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of ABCD3, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr1:94,045,555–94,046,076 372.6 kb Distal (>10kb) Multiome HiCAR 556
chr1:94,148,998–94,149,784 269.1 kb Distal (>10kb) Multiome 44
chr1:94,236,814–94,238,189 180.8 kb Distal (>10kb) Multiome 709
chr1:94,247,152–94,248,342 170.7 kb Distal (>10kb) Multiome 521
chr1:94,327,061–94,327,698 90.9 kb Distal (>10kb) Multiome 243
chr1:94,342,282–94,342,957 75.8 kb Distal (>10kb) Multiome 83
chr1:94,417,844–94,419,337 144 bp At TSS Multiome 948
chr1:94,540,914–94,542,577 123.4 kb Distal (>10kb) Multiome 726
chr1:94,570,815–94,571,430 152.7 kb Distal (>10kb) Multiome 129
chr1:94,572,275–94,573,057 154.2 kb Distal (>10kb) Multiome 73
chr1:94,657,564–94,658,605 239.7 kb Distal (>10kb) Multiome 208

Genome Browser

Genomic view of the ABCD3 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr1:94,035,555 – 94,668,605
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq