SCN5A
sodium voltage-gated channel alpha subunit 5 | CDCD2, CMPD2, HB1, HB2, HBBD, HH1, ICCD, IVF, LQT3, Nav1.5, PFHB1, SSS1, CMD1E

The protein encoded by this gene is an integral membrane protein and tetrodotoxin-resistant voltage-gated sodium channel subunit. This protein is found primarily in cardiac muscle and is responsible for the initial upstroke of the action potential in an electrocardiogram. Defects in this gene have been associated with long QT syndrome type 3 (LQT3), atrial fibrillation, cardiomyopathy, and Brugada syndrome 1, all autosomal dominant cardiac diseases. Alternative splicing results in several transcript variants encoding different isoforms. [provided by RefSeq, May 2022]

Biological processes 103 terms
AV node cell action potential (GO:0086016)AV node cell action potential (GO:0086016)AV node cell to bundle of His cell communication (GO:0086067)SA node cell action potential (GO:0086015)T-tubule (GO:0030315)T-tubule (GO:0030315)Z disc (GO:0030018)anchoring junction (GO:0070161)ankyrin binding (GO:0030506)atrial cardiac muscle cell action potential (GO:0086014)brainstem development (GO:0003360)bundle of His cell action potential (GO:0086043)bundle of His cell action potential (GO:0086043)calmodulin binding (GO:0005516)cardiac conduction system development (GO:0003161)cardiac muscle cell action potential involved in contraction (GO:0086002)cardiac muscle cell action potential involved in contraction (GO:0086002)cardiac muscle contraction (GO:0060048)cardiac ventricle development (GO:0003231)caveola (GO:0005901)caveola (GO:0005901)cell surface (GO:0009986)cell surface (GO:0009986)cellular response to calcium ion (GO:0071277)cerebellum development (GO:0021549)endoplasmic reticulum (GO:0005783)enzyme binding (GO:0019899)fibroblast growth factor binding (GO:0017134)intercalated disc (GO:0014704)intercalated disc (GO:0014704)intercalated disc (GO:0014704)lateral plasma membrane (GO:0016328)lateral plasma membrane (GO:0016328)membrane (GO:0016020)membrane (GO:0016020)membrane depolarization (GO:0051899)membrane depolarization during AV node cell action potential (GO:0086045)membrane depolarization during Purkinje myocyte cell action potential (GO:0086047)membrane depolarization during SA node cell action potential (GO:0086046)membrane depolarization during action potential (GO:0086010)membrane depolarization during atrial cardiac muscle cell action potential (GO:0098912)membrane depolarization during bundle of His cell action potential (GO:0086048)membrane depolarization during cardiac muscle cell action potential (GO:0086012)monoatomic cation channel activity (GO:0005261)monoatomic ion channel activity (GO:0005216)monoatomic ion transport (GO:0006811)nitric-oxide synthase binding (GO:0050998)odontogenesis of dentin-containing tooth (GO:0042475)perinuclear region of cytoplasm (GO:0048471)plasma membrane (GO:0005886)plasma membrane (GO:0005886)plasma membrane (GO:0005886)plasma membrane (GO:0005886)positive regulation of action potential (GO:0045760)positive regulation of epithelial cell proliferation (GO:0050679)positive regulation of sodium ion transport (GO:0010765)protein binding (GO:0005515)protein domain specific binding (GO:0019904)protein kinase binding (GO:0019901)regulation of atrial cardiac muscle cell membrane depolarization (GO:0060371)regulation of atrial cardiac muscle cell membrane depolarization (GO:0060371)regulation of atrial cardiac muscle cell membrane repolarization (GO:0060372)regulation of cardiac muscle cell contraction (GO:0086004)regulation of cardiac muscle contraction (GO:0055117)regulation of heart rate (GO:0002027)regulation of heart rate (GO:0002027)regulation of heart rate by cardiac conduction (GO:0086091)regulation of sodium ion transmembrane transport (GO:1902305)regulation of ventricular cardiac muscle cell membrane depolarization (GO:0060373)regulation of ventricular cardiac muscle cell membrane repolarization (GO:0060307)response to denervation involved in regulation of muscle adaptation (GO:0014894)sarcolemma (GO:0042383)scaffold protein binding (GO:0097110)scaffold protein binding (GO:0097110)sodium channel complex (GO:0034706)sodium ion transmembrane transport (GO:0035725)sodium ion transmembrane transport (GO:0035725)sodium ion transmembrane transport (GO:0035725)sodium ion transmembrane transport (GO:0035725)sodium ion transport (GO:0006814)sodium ion transport (GO:0006814)telencephalon development (GO:0021537)transmembrane transport (GO:0055085)transmembrane transporter binding (GO:0044325)ubiquitin protein ligase binding (GO:0031625)ubiquitin protein ligase binding (GO:0031625)ventricular cardiac muscle cell action potential (GO:0086005)voltage-gated sodium channel activity (GO:0005248)voltage-gated sodium channel activity (GO:0005248)voltage-gated sodium channel activity (GO:0005248)voltage-gated sodium channel activity (GO:0005248)voltage-gated sodium channel activity involved in AV node cell action potential (GO:0086060)voltage-gated sodium channel activity involved in Purkinje myocyte action potential (GO:0086062)voltage-gated sodium channel activity involved in SA node cell action potential (GO:0086063)voltage-gated sodium channel activity involved in SA node cell action potential (GO:0086063)voltage-gated sodium channel activity involved in bundle of His cell action potential (GO:0086061)voltage-gated sodium channel activity involved in cardiac muscle cell action potential (GO:0086006)voltage-gated sodium channel activity involved in cardiac muscle cell action potential (GO:0086006)voltage-gated sodium channel activity involved in cardiac muscle cell action potential (GO:0086006)voltage-gated sodium channel complex (GO:0001518)voltage-gated sodium channel complex (GO:0001518)voltage-gated sodium channel complex (GO:0001518)voltage-gated sodium channel complex (GO:0001518)
Expression (TPM)
SCN5A — as a Regulated Gene

TFs regulating SCN5A 0 TFs

Transcription factors with Perturb-seq knockdown data for SCN5A. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = SCN5A upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to SCN5A

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of SCN5A, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr3:38,028,710–38,030,184 620.0 kb Distal (>10kb) Multiome HiCAR 378
chr3:38,039,093–38,039,944 610.3 kb Distal (>10kb) Multiome HiCAR 357
chr3:38,452,852–38,456,220 196.0 kb Distal (>10kb) Multiome 971
chr3:38,495,771–38,496,881 153.3 kb Distal (>10kb) Multiome HiCAR 764
chr3:38,580,074–38,580,574 69.3 kb Distal (>10kb) Multiome 109
chr3:38,601,761–38,602,426 47.6 kb Distal (>10kb) Multiome 48
chr3:38,640,708–38,641,494 8.6 kb Proximal (<10kb) Multiome 182
chr3:38,649,012–38,650,212 5 bp At TSS Multiome 437
chr3:38,651,034–38,651,663 1.7 kb Proximal (<10kb) Multiome 351
chr3:38,655,779–38,656,034 6.1 kb Proximal (<10kb) 125
chr3:38,658,747–38,659,115 9.1 kb Proximal (<10kb) 28
chr3:38,669,439–38,670,183 20.1 kb Distal (>10kb) Multiome 85

Genome Browser

Genomic view of the SCN5A locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr3:38,018,710 – 38,680,183
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq