PRPS1
phosphoribosyl pyrophosphate synthetase 1 | CMTX5, DFNX1, PPRibP, PRS-I, DFN2

This gene encodes an enzyme that catalyzes the phosphoribosylation of ribose 5-phosphate to 5-phosphoribosyl-1-pyrophosphate, which is necessary for purine metabolism and nucleotide biosynthesis. Defects in this gene are a cause of phosphoribosylpyrophosphate synthetase superactivity, Charcot-Marie-Tooth disease X-linked recessive type 5 and Arts Syndrome. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Feb 2011]

Member of: DE-9 Developmental clusters: GC4
Biological processes 24 terms
Expression (TPM)
PRPS1 — as a Regulated Gene

TFs regulating PRPS1 0 TFs

Transcription factors with Perturb-seq knockdown data for PRPS1. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = PRPS1 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to PRPS1

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of PRPS1, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chrX:107,355,186–107,356,118 272.8 kb Distal (>10kb) Multiome 63
chrX:107,628,178–107,629,161 61 bp At TSS Multiome 409
chrX:107,654,846–107,655,657 26.8 kb Distal (>10kb) Multiome 393
chrX:107,731,822–107,732,545 103.7 kb Distal (>10kb) Multiome 347
chrX:107,736,604–107,737,564 108.6 kb Distal (>10kb) Multiome 303
chrX:107,825,723–107,827,075 197.9 kb Distal (>10kb) Multiome 369

Genome Browser

Genomic view of the PRPS1 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chrX:107,345,186 – 107,837,075
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq