MTHFD2
methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2, methenyltetrahydrofolate cyclohydrolase

This gene encodes a nuclear-encoded mitochondrial bifunctional enzyme with methylenetetrahydrofolate dehydrogenase and methenyltetrahydrofolate cyclohydrolase activities. The enzyme functions as a homodimer and is unique in its absolute requirement for magnesium and inorganic phosphate. Formation of the enzyme-magnesium complex allows binding of NAD. Alternative splicing results in two different transcripts, one protein-coding and the other not protein-coding. This gene has a pseudogene on chromosome 7. [provided by RefSeq, Mar 2009]

Developmental clusters: GC3
Biological processes 35 terms
catalytic activity (GO:0003824)extracellular region (GO:0005576)folic acid metabolic process (GO:0046655)folic acid metabolic process (GO:0046655)formate biosynthetic process (GO:0015943)magnesium ion binding (GO:0000287)magnesium ion binding (GO:0000287)methenyltetrahydrofolate cyclohydrolase activity (GO:0004477)methenyltetrahydrofolate cyclohydrolase activity (GO:0004477)methenyltetrahydrofolate cyclohydrolase activity (GO:0004477)methenyltetrahydrofolate cyclohydrolase activity (GO:0004477)methenyltetrahydrofolate cyclohydrolase activity (GO:0004477)methylenetetrahydrofolate dehydrogenase (NAD+) activity (GO:0004487)methylenetetrahydrofolate dehydrogenase (NAD+) activity (GO:0004487)methylenetetrahydrofolate dehydrogenase (NAD+) activity (GO:0004487)methylenetetrahydrofolate dehydrogenase (NAD+) activity (GO:0004487)methylenetetrahydrofolate dehydrogenase (NAD+) activity (GO:0004487)methylenetetrahydrofolate dehydrogenase (NADP+) activity (GO:0004488)methylenetetrahydrofolate dehydrogenase (NADP+) activity (GO:0004488)methylenetetrahydrofolate dehydrogenase (NADP+) activity (GO:0004488)methylenetetrahydrofolate dehydrogenase (NADP+) activity (GO:0004488)mitochondrial matrix (GO:0005759)mitochondrial matrix (GO:0005759)mitochondrial matrix (GO:0005759)mitochondrion (GO:0005739)mitochondrion (GO:0005739)mitochondrion (GO:0005739)mitochondrion (GO:0005739)mitochondrion (GO:0005739)phosphate ion binding (GO:0042301)phosphate ion binding (GO:0042301)protein binding (GO:0005515)tetrahydrofolate interconversion (GO:0035999)tetrahydrofolate interconversion (GO:0035999)tetrahydrofolate metabolic process (GO:0046653)
Expression (TPM)
MTHFD2 — as a Regulated Gene

TFs regulating MTHFD2 0 TFs

Transcription factors with Perturb-seq knockdown data for MTHFD2. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = MTHFD2 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to MTHFD2

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of MTHFD2, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr2:73,921,096–73,921,666 277.2 kb Distal (>10kb) Multiome 284
chr2:73,926,648–73,927,193 271.7 kb Distal (>10kb) Multiome 961
chr2:73,981,145–73,981,910 217.0 kb Distal (>10kb) Multiome 483
chr2:73,983,451–73,985,871 213.3 kb Distal (>10kb) Multiome 821
chr2:74,002,059–74,003,348 195.9 kb Distal (>10kb) Multiome 514
chr2:74,008,705–74,009,321 189.6 kb Distal (>10kb) Multiome 142
chr2:74,026,198–74,026,578 172.2 kb Distal (>10kb) Multiome 88
chr2:74,119,987–74,120,643 78.2 kb Distal (>10kb) Multiome 969
chr2:74,147,573–74,148,843 50.6 kb Distal (>10kb) Multiome 884
chr2:74,178,147–74,179,324 19.7 kb Distal (>10kb) Multiome 869
chr2:74,187,993–74,188,519 10.4 kb Distal (>10kb) Multiome 192
chr2:74,198,074–74,199,486 66 bp At TSS Multiome 1098
chr2:74,261,293–74,261,813 63.0 kb Distal (>10kb) Multiome 184
chr2:74,374,253–74,375,246 176.1 kb Distal (>10kb) Multiome 158
chr2:74,379,653–74,380,438 181.4 kb Distal (>10kb) Multiome 229
chr2:74,391,129–74,392,484 193.3 kb Distal (>10kb) Multiome 876
chr2:74,421,273–74,422,464 223.1 kb Distal (>10kb) Multiome 756
chr2:74,426,172–74,426,842 228.0 kb Distal (>10kb) Multiome 88
chr2:74,440,246–74,442,723 243.5 kb Distal (>10kb) Multiome 1050
chr2:74,454,612–74,455,413 256.4 kb Distal (>10kb) Multiome 982
chr2:74,457,177–74,459,169 259.7 kb Distal (>10kb) Multiome 934
chr2:74,464,912–74,465,776 266.8 kb Distal (>10kb) Multiome 842
chr2:74,472,106–74,473,059 274.0 kb Distal (>10kb) Multiome 1071
chr2:74,481,955–74,483,673 284.5 kb Distal (>10kb) Multiome 1031
chr2:74,497,707–74,500,027 299.6 kb Distal (>10kb) Multiome 553

Genome Browser

Genomic view of the MTHFD2 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr2:73,911,096 – 74,510,027
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq