EHHADH
enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase | ECHD

The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Oct 2009]

Member of: DE-4 DE-4.6 Developmental clusters: GC7
Biological processes 42 terms
(3S)-3-hydroxyacyl-CoA dehydrogenase (NAD+) activity (GO:0003857)(3S)-3-hydroxyacyl-CoA dehydrogenase (NAD+) activity (GO:0003857)(3S)-3-hydroxyacyl-CoA dehydrogenase (NAD+) activity (GO:0003857)(3S)-3-hydroxyacyl-CoA dehydrogenase (NAD+) activity (GO:0003857)(3S)-3-hydroxyacyl-CoA dehydrogenase (NAD+) activity (GO:0003857)(3S)-3-hydroxyacyl-CoA dehydrogenase (NAD+) activity (GO:0003857)3-hydroxyacyl-CoA dehydratase activity (GO:0018812)3-hydroxyacyl-CoA dehydratase activity (GO:0018812)NAD+ binding (GO:0070403)catalytic activity (GO:0003824)cytosol (GO:0005829)cytosol (GO:0005829)delta(3)-delta(2)-enoyl-CoA isomerase activity (GO:0004165)delta(3)-delta(2)-enoyl-CoA isomerase activity (GO:0004165)enoyl-CoA hydratase activity (GO:0004300)enoyl-CoA hydratase activity (GO:0004300)enoyl-CoA hydratase activity (GO:0004300)enoyl-CoA hydratase activity (GO:0004300)enzyme binding (GO:0019899)enzyme binding (GO:0019899)fatty acid beta-oxidation (GO:0006635)fatty acid beta-oxidation (GO:0006635)fatty acid beta-oxidation (GO:0006635)fatty acid beta-oxidation (GO:0006635)fatty acid beta-oxidation (GO:0006635)fatty acid beta-oxidation using acyl-CoA oxidase (GO:0033540)fatty acid beta-oxidation using acyl-CoA oxidase (GO:0033540)fatty acid biosynthetic process (GO:0006633)fatty acid metabolic process (GO:0006631)intramolecular oxidoreductase activity, transposing C=C bonds (GO:0016863)intramolecular oxidoreductase activity, transposing C=C bonds (GO:0016863)long-chain (3S)-3-hydroxyacyl-CoA dehydrogenase (NAD+) activity (GO:0016509)oxidoreductase activity (GO:0016491)oxidoreductase activity, acting on the CH-OH group of donors, NAD or NADP as acceptor (GO:0016616)peroxisomal matrix (GO:0005782)peroxisomal matrix (GO:0005782)peroxisome (GO:0005777)peroxisome (GO:0005777)peroxisome (GO:0005777)peroxisome (GO:0005777)peroxisome (GO:0005777)protein binding (GO:0005515)
Expression (TPM)
EHHADH — as a Regulated Gene

TFs regulating EHHADH 0 TFs

Transcription factors with Perturb-seq knockdown data for EHHADH. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = EHHADH upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to EHHADH

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of EHHADH, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr3:185,152,390–185,153,792 101.2 kb Distal (>10kb) Multiome 589
chr3:185,249,926–185,250,485 3.9 kb Proximal (<10kb) Multiome 51
chr3:185,253,856–185,254,366 at TSS At TSS 650
chr3:185,267,961–185,268,947 14.5 kb Distal (>10kb) Multiome 258
chr3:185,269,944–185,270,809 16.5 kb Distal (>10kb) Multiome 180
chr3:185,282,769–185,283,294 28.9 kb Distal (>10kb) Multiome 660
chr3:185,372,493–185,373,188 118.7 kb Distal (>10kb) Multiome 60
chr3:185,498,399–185,499,479 245.0 kb Distal (>10kb) Multiome 1024

Genome Browser

Genomic view of the EHHADH locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr3:185,142,390 – 185,509,479
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq