SOD1
superoxide dismutase 1 | IPOA, ALS, ALS1

The protein encoded by this gene binds copper and zinc ions and is one of two isozymes responsible for destroying free superoxide radicals in the body. The encoded isozyme is a soluble cytoplasmic protein, acting as a homodimer to convert naturally-occuring but harmful superoxide radicals to molecular oxygen and hydrogen peroxide. The other isozyme is a mitochondrial protein. In addition, this protein contains an antimicrobial peptide that displays antibacterial, antifungal, and anti-MRSA activity against E. coli, E. faecalis, S. aureus, S. aureus MRSA LPV+, S. agalactiae, and yeast C. krusei. Mutations in this gene have been implicated as causes of familial amyotrophic lateral sclerosis. Rare transcript variants have been reported for this gene. [provided by RefSeq, Jul 2020]

Member of: DE-1 DE-1.47 Developmental clusters: GC5
Biological processes 115 terms
anterograde axonal transport (GO:0008089)anterograde axonal transport (GO:0008089)auditory receptor cell stereocilium organization (GO:0060088)axon cytoplasm (GO:1904115)cellular response to ATP (GO:0071318)cellular response to cadmium ion (GO:0071276)cellular response to oxidative stress (GO:0034599)cellular response to potassium ion (GO:0035865)copper ion binding (GO:0005507)copper ion binding (GO:0005507)copper ion binding (GO:0005507)cytoplasm (GO:0005737)cytoplasm (GO:0005737)cytoplasmic vesicle (GO:0031410)cytosol (GO:0005829)cytosol (GO:0005829)cytosol (GO:0005829)dendrite cytoplasm (GO:0032839)dense core granule (GO:0031045)embryo implantation (GO:0007566)embryo implantation (GO:0007566)enzyme binding (GO:0019899)extracellular exosome (GO:0070062)extracellular region (GO:0005576)extracellular region (GO:0005576)extracellular region (GO:0005576)glutathione metabolic process (GO:0006749)heart contraction (GO:0060047)hydrogen peroxide biosynthetic process (GO:0050665)hydrogen peroxide biosynthetic process (GO:0050665)hydrogen peroxide biosynthetic process (GO:0050665)identical protein binding (GO:0042802)intracellular iron ion homeostasis (GO:0006879)locomotory behavior (GO:0007626)lysosome (GO:0005764)metal ion binding (GO:0046872)mitochondrial intermembrane space (GO:0005758)mitochondrial matrix (GO:0005759)mitochondrion (GO:0005739)mitochondrion (GO:0005739)mitochondrion (GO:0005739)muscle cell cellular homeostasis (GO:0046716)myeloid cell homeostasis (GO:0002262)negative regulation of apoptotic process (GO:0043066)negative regulation of inflammatory response (GO:0050728)negative regulation of neuron apoptotic process (GO:0043524)neurofilament cytoskeleton organization (GO:0060052)neuronal cell body (GO:0043025)neuronal cell body (GO:0043025)nucleoplasm (GO:0005654)nucleus (GO:0005634)nucleus (GO:0005634)nucleus (GO:0005634)nucleus (GO:0005634)ovarian follicle development (GO:0001541)peripheral nervous system myelin maintenance (GO:0032287)peroxisome (GO:0005777)peroxisome (GO:0005777)peroxisome (GO:0005777)peroxisome (GO:0005777)placenta development (GO:0001890)plasma membrane (GO:0005886)positive regulation of MAPK cascade (GO:0043410)positive regulation of apoptotic process (GO:0043065)positive regulation of cytokine production (GO:0001819)positive regulation of oxidative stress-induced intrinsic apoptotic signaling pathway (GO:1902177)positive regulation of phagocytosis (GO:0050766)positive regulation of superoxide anion generation (GO:0032930)protein binding (GO:0005515)protein homodimerization activity (GO:0042803)protein phosphatase 2B binding (GO:0030346)protein phosphatase 2B binding (GO:0030346)protein-containing complex (GO:0032991)protein-containing complex (GO:0032991)protein-folding chaperone binding (GO:0051087)reactive oxygen species metabolic process (GO:0072593)regulation of GTPase activity (GO:0043087)regulation of T cell differentiation in thymus (GO:0033081)regulation of blood pressure (GO:0008217)regulation of mitochondrial membrane potential (GO:0051881)regulation of multicellular organism growth (GO:0040014)regulation of organ growth (GO:0046620)relaxation of vascular associated smooth muscle (GO:0060087)removal of superoxide radicals (GO:0019430)removal of superoxide radicals (GO:0019430)removal of superoxide radicals (GO:0019430)removal of superoxide radicals (GO:0019430)removal of superoxide radicals (GO:0019430)response to amphetamine (GO:0001975)response to antipsychotic drug (GO:0097332)response to axon injury (GO:0048678)response to carbon monoxide (GO:0034465)response to copper ion (GO:0046688)response to ethanol (GO:0045471)response to heat (GO:0009408)response to hydrogen peroxide (GO:0042542)response to nutrient levels (GO:0031667)response to oxidative stress (GO:0006979)response to superoxide (GO:0000303)retina homeostasis (GO:0001895)retrograde axonal transport (GO:0008090)retrograde axonal transport (GO:0008090)secretory granule (GO:0030141)sensory perception of sound (GO:0007605)small GTPase binding (GO:0031267)spermatogenesis (GO:0007283)superoxide dismutase activity (GO:0004784)superoxide dismutase activity (GO:0004784)superoxide dismutase activity (GO:0004784)superoxide metabolic process (GO:0006801)superoxide metabolic process (GO:0006801)superoxide metabolic process (GO:0006801)thymus development (GO:0048538)transmission of nerve impulse (GO:0019226)zinc ion binding (GO:0008270)
Expression (TPM)
SOD1 — as a Regulated Gene

TFs regulating SOD1 0 TFs

Transcription factors with Perturb-seq knockdown data for SOD1. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = SOD1 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to SOD1

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of SOD1, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr21:31,524,028–31,524,533 135.3 kb Distal (>10kb) Multiome 76
chr21:31,555,561–31,556,422 103.7 kb Distal (>10kb) Multiome 195
chr21:31,557,394–31,560,223 100.4 kb Distal (>10kb) Multiome 556
chr21:31,659,244–31,660,576 25 bp At TSS Multiome 974
chr21:31,730,700–31,732,702 72.5 kb Distal (>10kb) Multiome 872
chr21:31,872,362–31,874,730 213.3 kb Distal (>10kb) Multiome 609

Genome Browser

Genomic view of the SOD1 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr21:31,514,028 – 31,884,730
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq