SETX
senataxin | AOA2, KIAA0625, STEX, Sen1, ALS4, SCAR1

This gene encodes a protein named for its homology to the Sen1p protein of fungi which has RNA helicase activity encoded by a domain at the C-terminal end of the protein. The protein encoded by this gene contains a DNA/RNA helicase domain at its C-terminal end which suggests that it may be involved in both DNA and RNA processing. Mutations in this gene have been associated with ataxia-ocular apraxia-2 (AOA2) and an autosomal dominant form of juvenile amyotrophic lateral sclerosis (ALS4). [provided by RefSeq, Jul 2008]

Member of: DE-2 DE-2.7
Biological processes 44 terms
5'-3' DNA helicase activity (GO:0043139)5'-3' DNA/RNA helicase activity (GO:0033678)ATP hydrolysis activity (GO:0016887)DNA binding (GO:0003677)DNA damage response (GO:0006974)DNA helicase activity (GO:0003678)DNA helicase activity (GO:0003678)DNA-templated transcription termination (GO:0006353)DNA-templated transcription termination (GO:0006353)DNA-templated transcription termination (GO:0006353)DNA/RNA helicase activity (GO:0033677)RNA binding (GO:0003723)RNA helicase activity (GO:0003724)RNA processing (GO:0006396)axon (GO:0030424)axon (GO:0030424)cellular response to hydrogen peroxide (GO:0070301)cellular response to oxidative stress (GO:0034599)chromosome (GO:0005694)chromosome, telomeric region (GO:0000781)cytoplasm (GO:0005737)cytoplasm (GO:0005737)double-strand break repair (GO:0006302)growth cone (GO:0030426)growth cone (GO:0030426)helicase activity (GO:0004386)identical protein binding (GO:0042802)mRNA splice site recognition (GO:0006376)nuclear chromosome (GO:0000228)nucleolus (GO:0005730)nucleoplasm (GO:0005654)nucleoplasm (GO:0005654)nucleus (GO:0005634)nucleus (GO:0005634)positive regulation of DNA-templated transcription initiation (GO:2000144)positive regulation of RNA splicing (GO:0033120)positive regulation of neuron projection development (GO:0010976)positive regulation of termination of DNA-templated transcription (GO:0060566)positive regulation of termination of RNA polymerase II transcription, poly(A)-coupled (GO:2000806)positive regulation of transcription by RNA polymerase II (GO:0045944)protein binding (GO:0005515)termination of RNA polymerase II transcription (GO:0006369)transcription termination site sequence-specific DNA binding (GO:0001147)transcription termination site sequence-specific DNA binding (GO:0001147)
Expression (TPM)
SETX — as a Regulated Gene

TFs regulating SETX 0 TFs

Transcription factors with Perturb-seq knockdown data for SETX. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = SETX upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to SETX

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of SETX, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr9:132,079,578–132,080,009 275.1 kb Distal (>10kb) Multiome 537
chr9:132,239,978–132,242,316 113.7 kb Distal (>10kb) Multiome 555
chr9:132,259,091–132,259,539 95.6 kb Distal (>10kb) Multiome 443
chr9:132,354,395–132,355,656 124 bp At TSS Multiome 895
chr9:132,409,879–132,410,471 55.1 kb Distal (>10kb) Multiome 293
chr9:132,411,065–132,411,553 56.3 kb Distal (>10kb) Multiome 342
chr9:132,582,095–132,582,589 227.2 kb Distal (>10kb) Multiome 938

Genome Browser

Genomic view of the SETX locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr9:132,069,578 – 132,592,589
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq