MCCC2
methylcrotonyl-CoA carboxylase subunit 2 | MCCB, MCCCβ

This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. Alternative splicing results in multiple transcript variants encoding distinct isoforms. [provided by RefSeq, May 2018]

Member of: DE-2 DE-2.4
Biological processes 25 terms
Expression (TPM)
MCCC2 — as a Regulated Gene

TFs regulating MCCC2 0 TFs

Transcription factors with Perturb-seq knockdown data for MCCC2. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = MCCC2 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to MCCC2

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of MCCC2, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr5:71,455,476–71,456,380 131.6 kb Distal (>10kb) Multiome 791
chr5:71,586,567–71,588,044 58 bp At TSS Multiome 835

Genome Browser

Genomic view of the MCCC2 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr5:71,445,476 – 71,598,044
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq