HPS5
HPS5 biogenesis of lysosomal organelles complex 2 subunit 2 | AIBP63, BLOC2S2, RU2

This gene encodes a protein that may play a role in organelle biogenesis associated with melanosomes, platelet dense granules, and lysosomes. This protein interacts with Hermansky-Pudlak syndrome 6 protein and may interact with the cytoplasmic domain of integrin, alpha-3. Mutations in this gene are associated with Hermansky-Pudlak syndrome type 5. Multiple transcript variants encoding two distinct isoforms have been identified for this gene. [provided by RefSeq, Jul 2008]

Member of: DE-10 DE-10.3
Biological processes 9 terms
Expression (TPM)
HPS5 — as a Regulated Gene

TFs regulating HPS5 0 TFs

Transcription factors with Perturb-seq knockdown data for HPS5. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = HPS5 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to HPS5

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of HPS5, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr11:18,105,744–18,106,263 216.1 kb Distal (>10kb) Multiome 873
chr11:18,318,016–18,318,522 3.9 kb Proximal (<10kb) Multiome 49
chr11:18,321,766–18,322,926 200 bp At TSS Multiome 1044
chr11:18,393,759–18,396,665 74.1 kb Distal (>10kb) Multiome 1203
chr11:18,526,292–18,527,325 204.7 kb Distal (>10kb) Multiome 1012
chr11:18,588,293–18,589,047 266.6 kb Distal (>10kb) Multiome 837

Genome Browser

Genomic view of the HPS5 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr11:18,095,744 – 18,599,047
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq