EXT1
exostosin glycosyltransferase 1 | ttv, LGCR, LGS

This gene encodes an endoplasmic reticulum-resident type II transmembrane glycosyltransferase involved in the chain elongation step of heparan sulfate biosynthesis. Mutations in this gene cause the type I form of multiple exostoses. [provided by RefSeq, Jul 2008]

Member of: DE-2 DE-2.19
Biological processes 39 terms
Golgi apparatus (GO:0005794)Golgi apparatus (GO:0005794)Golgi apparatus (GO:0005794)Golgi apparatus (GO:0005794)Golgi apparatus (GO:0005794)Golgi membrane (GO:0000139)Golgi membrane (GO:0000139)N-acetylglucosaminyl-proteoglycan 4-beta-glucuronosyltransferase activity (GO:0050509)N-acetylglucosaminyl-proteoglycan 4-beta-glucuronosyltransferase activity (GO:0050509)N-acetylglucosaminyl-proteoglycan 4-beta-glucuronosyltransferase activity (GO:0050509)N-acetylglucosaminyl-proteoglycan 4-beta-glucuronosyltransferase activity (GO:0050509)acetylglucosaminyltransferase activity (GO:0008375)catalytic complex (GO:1902494)endoplasmic reticulum (GO:0005783)endoplasmic reticulum (GO:0005783)endoplasmic reticulum membrane (GO:0005789)endoplasmic reticulum membrane (GO:0005789)endoplasmic reticulum membrane (GO:0005789)glucuronosyl-N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase activity (GO:0050508)glucuronosyl-N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase activity (GO:0050508)glucuronosyl-N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase activity (GO:0050508)glucuronosyl-N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase activity (GO:0050508)glucuronosyl-N-acetylglucosaminyl-proteoglycan 4-alpha-N-acetylglucosaminyltransferase activity (GO:0050508)glucuronosyltransferase activity (GO:0015020)glycoprotein biosynthetic process (GO:0009101)glycosaminoglycan biosynthetic process (GO:0006024)glycosyltransferase activity (GO:0016757)heparan sulfate N-acetylglucosaminyltransferase activity (GO:0042328)heparan sulfate proteoglycan biosynthetic process (GO:0015012)heparan sulfate proteoglycan biosynthetic process (GO:0015012)heparan sulfate proteoglycan biosynthetic process (GO:0015012)heparan sulfate proteoglycan biosynthetic process (GO:0015012)membrane (GO:0016020)ossification (GO:0001503)ossification (GO:0001503)polysaccharide biosynthetic process (GO:0000271)protein binding (GO:0005515)protein heterodimerization activity (GO:0046982)protein homodimerization activity (GO:0042803)
Expression (TPM)
EXT1 — as a Regulated Gene

TFs regulating EXT1 0 TFs

Transcription factors with Perturb-seq knockdown data for EXT1. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = EXT1 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to EXT1

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of EXT1, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr8:117,958,893–117,959,598 152.7 kb Distal (>10kb) Multiome HiCAR 208
chr8:118,073,868–118,075,439 37.3 kb Distal (>10kb) Multiome 407
chr8:118,101,378–118,102,179 9.6 kb Proximal (<10kb) 187
chr8:118,103,226–118,103,830 8.0 kb Proximal (<10kb) 126
chr8:118,108,881–118,109,294 2.5 kb Proximal (<10kb) 323
chr8:118,109,662–118,110,359 1.5 kb Proximal (<10kb) 227
chr8:118,110,761–118,113,665 81 bp At TSS Multiome 813
chr8:118,116,241–118,116,630 4.4 kb Proximal (<10kb) 122
chr8:118,117,996–118,118,499 6.2 kb Proximal (<10kb) 48
chr8:118,120,654–118,120,935 8.8 kb Proximal (<10kb) 167

Genome Browser

Genomic view of the EXT1 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr8:117,948,893 – 118,130,935
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq