DKC1
dyskerin pseudouridine synthase 1 | Cbf5, NAP57, NOLA4, XAP101, dyskerin, DKC

This gene functions in two distinct complexes. It plays an active role in telomerase stabilization and maintenance, as well as recognition of snoRNAs containing H/ACA sequences which provides stability during biogenesis and assembly into H/ACA small nucleolar RNA ribonucleoproteins (snoRNPs). This gene is highly conserved and widely expressed, and may play additional roles in nucleo-cytoplasmic shuttling, DNA damage response, and cell adhesion. Mutations have been associated with X-linked dyskeratosis congenita. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2014]

Member of: DE-1 DE-1.18 Developmental clusters: GC4
Biological processes 50 terms
Cajal body (GO:0015030)RNA binding (GO:0003723)RNA binding (GO:0003723)RNA binding (GO:0003723)RNA binding (GO:0003723)RNA modification (GO:0009451)RNA processing (GO:0006396)RNA processing (GO:0006396)box H/ACA scaRNP complex (GO:0072589)box H/ACA sno(s)RNA 3'-end processing (GO:0000495)box H/ACA snoRNA binding (GO:0034513)box H/ACA snoRNP complex (GO:0031429)box H/ACA snoRNP complex (GO:0031429)box H/ACA snoRNP complex (GO:0031429)box H/ACA telomerase RNP complex (GO:0090661)box H/ACA telomerase RNP complex (GO:0090661)cytoplasm (GO:0005737)enzyme-directed rRNA pseudouridine synthesis (GO:0000455)fibrillar center (GO:0001650)mRNA pseudouridine synthesis (GO:1990481)nucleolus (GO:0005730)nucleolus (GO:0005730)nucleoplasm (GO:0005654)nucleoplasm (GO:0005654)nucleus (GO:0005634)positive regulation of telomerase RNA localization to Cajal body (GO:1904874)positive regulation of telomere maintenance via telomerase (GO:0032212)positive regulation of telomere maintenance via telomerase (GO:0032212)protein binding (GO:0005515)protein localization to Cajal body (GO:1904867)pseudouridine synthase activity (GO:0009982)pseudouridine synthase activity (GO:0009982)pseudouridine synthase activity (GO:0009982)pseudouridine synthesis (GO:0001522)rRNA processing (GO:0006364)rRNA pseudouridine synthesis (GO:0031118)rRNA pseudouridine synthesis (GO:0031118)regulation of telomerase RNA localization to Cajal body (GO:1904872)scaRNA localization to Cajal body (GO:0090666)snRNA pseudouridine synthesis (GO:0031120)telomerase RNA binding (GO:0070034)telomerase RNA stabilization (GO:0090669)telomerase activity (GO:0003720)telomerase activity (GO:0003720)telomerase holoenzyme complex (GO:0005697)telomerase holoenzyme complex (GO:0005697)telomere maintenance via telomerase (GO:0007004)telomere maintenance via telomerase (GO:0007004)telomere maintenance via telomerase (GO:0007004)telomere maintenance via telomerase (GO:0007004)
Expression (TPM)
DKC1 — as a Regulated Gene

TFs regulating DKC1 0 TFs

Transcription factors with Perturb-seq knockdown data for DKC1. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = DKC1 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to DKC1

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of DKC1, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chrX:154,478,385–154,479,590 283.7 kb Distal (>10kb) Multiome 707
chrX:154,486,385–154,487,035 276.0 kb Distal (>10kb) Multiome 437
chrX:154,490,259–154,491,245 272.0 kb Distal (>10kb) Multiome 567
chrX:154,515,811–154,517,059 246.4 kb Distal (>10kb) Multiome 590
chrX:154,546,514–154,547,906 215.5 kb Distal (>10kb) Multiome 691
chrX:154,762,385–154,763,339 21 bp At TSS Multiome 675
chrX:154,805,199–154,805,850 42.8 kb Distal (>10kb) Multiome 481
chrX:155,026,631–155,027,442 264.2 kb Distal (>10kb) Multiome 744

Genome Browser

Genomic view of the DKC1 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chrX:154,468,385 – 155,037,442
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq