DERL1
derlin 1 | DER-1, DER1, FLJ13784, MGC3067, PRO2577, derlin-1

The protein encoded by this gene is a member of the derlin family. Members of this family participate in the ER-associated degradation response and retrotranslocate misfolded or unfolded proteins from the ER lumen to the cytosol for proteasomal degradation. This protein recognizes substrate in the ER and works in a complex to retrotranslocate it across the ER membrane into the cytosol. This protein may select cystic fibrosis transmembrane conductance regulator protein (CFTR) for degradation as well as unfolded proteins in Alzheimer's disease. Alternative splicing results in multiple transcript variants that encode different protein isoforms. [provided by RefSeq, Aug 2012]

Member of: DE-1 Developmental clusters: GC1
Biological processes 45 terms
ATPase binding (GO:0051117)Derlin-1 retrotranslocation complex (GO:0036513)Derlin-1-VIMP complex (GO:0036502)ERAD pathway (GO:0036503)ERAD pathway (GO:0036503)ERAD pathway (GO:0036503)ERAD pathway (GO:0036503)MHC class I protein binding (GO:0042288)cellular response to misfolded protein (GO:0071218)cellular response to stress (GO:0033554)cytoplasm (GO:0005737)early endosome (GO:0005769)endoplasmic reticulum (GO:0005783)endoplasmic reticulum (GO:0005783)endoplasmic reticulum (GO:0005783)endoplasmic reticulum membrane (GO:0005789)endoplasmic reticulum membrane (GO:0005789)endoplasmic reticulum membrane (GO:0005789)endoplasmic reticulum membrane (GO:0005789)endoplasmic reticulum membrane (GO:0005789)endoplasmic reticulum quality control compartment (GO:0044322)endoplasmic reticulum unfolded protein response (GO:0030968)endoplasmic reticulum unfolded protein response (GO:0030968)establishment of protein localization (GO:0045184)identical protein binding (GO:0042802)late endosome (GO:0005770)membrane (GO:0016020)membrane (GO:0016020)positive regulation of protein ubiquitination (GO:0031398)protease binding (GO:0002020)proteasomal protein catabolic process (GO:0010498)proteasome-mediated ubiquitin-dependent protein catabolic process (GO:0043161)protein binding (GO:0005515)protein destabilization (GO:0031648)protein-containing complex binding (GO:0044877)response to unfolded protein (GO:0006986)retrograde protein transport, ER to cytosol (GO:0030970)retrograde protein transport, ER to cytosol (GO:0030970)retrograde protein transport, ER to cytosol (GO:0030970)signal recognition particle binding (GO:0005047)signal recognition particle binding (GO:0005047)signaling receptor activity (GO:0038023)ubiquitin protein ligase binding (GO:0031625)ubiquitin-dependent protein catabolic process (GO:0006511)ubiquitin-specific protease binding (GO:1990381)
Expression (TPM)
DERL1 — as a Regulated Gene

TFs regulating DERL1 0 TFs

Transcription factors with Perturb-seq knockdown data for DERL1. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = DERL1 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to DERL1

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of DERL1, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr8:122,686,468–122,687,541 355.3 kb Distal (>10kb) Multiome HiCAR 263
chr8:122,780,039–122,780,999 261.9 kb Distal (>10kb) Multiome 860
chr8:122,781,087–122,783,557 259.2 kb Distal (>10kb) Multiome 793
chr8:122,837,253–122,838,328 204.3 kb Distal (>10kb) Multiome 291
chr8:123,041,536–123,042,890 21 bp At TSS Multiome 925
chr8:123,065,582–123,066,386 23.8 kb Distal (>10kb) Multiome 354
chr8:123,072,367–123,073,561 30.3 kb Distal (>10kb) Multiome 858
chr8:123,156,604–123,157,953 115.0 kb Distal (>10kb) Multiome 1083
chr8:123,160,441–123,161,547 118.4 kb Distal (>10kb) Multiome 590
chr8:123,205,121–123,205,789 163.2 kb Distal (>10kb) Multiome 298
chr8:123,207,081–123,207,716 165.1 kb Distal (>10kb) Multiome 96
chr8:123,235,684–123,236,295 193.7 kb Distal (>10kb) Multiome 110
chr8:123,240,791–123,241,581 199.1 kb Distal (>10kb) Multiome 784
chr8:123,273,286–123,275,625 232.4 kb Distal (>10kb) Multiome 970

Genome Browser

Genomic view of the DERL1 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr8:122,676,468 – 123,285,625
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq