ATP7B
ATPase copper transporting beta | WND

This gene is a member of the P-type cation transport ATPase family and encodes a protein with several membrane-spanning domains, an ATPase consensus sequence, a hinge domain, a phosphorylation site, and at least 2 putative copper-binding sites. This protein is a monomer, and functions as a copper-transporting ATPase which exports copper out of the cells, such as the efflux of hepatic copper into the bile. Alternate transcriptional splice variants, encoding different isoforms with distinct cellular localizations, have been characterized. Mutations in this gene have been associated with Wilson disease which is characterized by copper accumulation. [provided by RefSeq, Dec 2019]

Member of: DE-2 DE-2.45 Developmental clusters: GC7
Biological processes 50 terms
ATP binding (GO:0005524)ATP binding (GO:0005524)ATP hydrolysis activity (GO:0016887)ATPase-coupled monoatomic cation transmembrane transporter activity (GO:0019829)Golgi apparatus (GO:0005794)Golgi apparatus (GO:0005794)Golgi membrane (GO:0000139)Golgi membrane (GO:0000139)P-type monovalent copper transporter activity (GO:0140581)P-type monovalent copper transporter activity (GO:0140581)P-type monovalent copper transporter activity (GO:0140581)P-type monovalent copper transporter activity (GO:0140581)P-type monovalent copper transporter activity (GO:0140581)basolateral plasma membrane (GO:0016323)cellular detoxification of copper ion (GO:1990880)copper ion binding (GO:0005507)copper ion binding (GO:0005507)copper ion binding (GO:0005507)copper ion export (GO:0060003)copper ion import (GO:0015677)copper ion transmembrane transporter activity (GO:0005375)copper ion transmembrane transporter activity (GO:0005375)copper ion transport (GO:0006825)copper ion transport (GO:0006825)copper ion transport (GO:0006825)cytoplasm (GO:0005737)cytoplasmic vesicle (GO:0031410)intracellular copper ion homeostasis (GO:0006878)intracellular copper ion homeostasis (GO:0006878)late endosome (GO:0005770)late endosome (GO:0005770)membrane (GO:0016020)membrane (GO:0016020)metal ion binding (GO:0046872)mitochondrion (GO:0005739)mitochondrion (GO:0005739)monoatomic cation transport (GO:0006812)monoatomic ion transmembrane transport (GO:0034220)nucleotide binding (GO:0000166)perinuclear region of cytoplasm (GO:0048471)plasma membrane (GO:0005886)plasma membrane (GO:0005886)protein binding (GO:0005515)response to copper ion (GO:0046688)response to copper ion (GO:0046688)trans-Golgi network (GO:0005802)trans-Golgi network (GO:0005802)trans-Golgi network membrane (GO:0032588)trans-Golgi network membrane (GO:0032588)xenobiotic detoxification by transmembrane export across the plasma membrane (GO:1990961)
Expression (TPM)
ATP7B — as a Regulated Gene

TFs regulating ATP7B 0 TFs

Transcription factors with Perturb-seq knockdown data for ATP7B. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = ATP7B upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to ATP7B

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of ATP7B, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr13:51,795,081–51,795,749 216.6 kb Distal (>10kb) Multiome 50
chr13:51,803,129–51,804,466 208.1 kb Distal (>10kb) Multiome 844
chr13:51,997,545–51,998,310 14.1 kb Distal (>10kb) Multiome 461
chr13:52,011,124–52,012,698 78 bp At TSS Multiome 960
chr13:52,128,284–52,129,389 116.9 kb Distal (>10kb) Multiome 598
chr13:52,159,155–52,160,117 147.4 kb Distal (>10kb) Multiome 831
chr13:52,194,155–52,194,839 182.4 kb Distal (>10kb) Multiome 888
chr13:52,195,279–52,195,948 183.6 kb Distal (>10kb) Multiome 267

Genome Browser

Genomic view of the ATP7B locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr13:51,785,081 – 52,205,948
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq