AFG3L2
AFG3 like matrix AAA peptidase subunit 2 | SPAX5, SCA28

This gene encodes a protein localized in mitochondria and closely related to paraplegin. The paraplegin gene is responsible for an autosomal recessive form of hereditary spastic paraplegia. This gene is a candidate gene for other hereditary spastic paraplegias or neurodegenerative disorders. [provided by RefSeq, Jul 2008]

Member of: DE-4 Developmental clusters: GC4
Biological processes 47 terms
ATP binding (GO:0005524)ATP hydrolysis activity (GO:0016887)ATP hydrolysis activity (GO:0016887)ATP-dependent peptidase activity (GO:0004176)axonogenesis (GO:0007409)calcium import into the mitochondrion (GO:0036444)cellular response to glutathione (GO:0072753)m-AAA complex (GO:0005745)m-AAA complex (GO:0005745)m-AAA complex (GO:0005745)membrane (GO:0016020)membrane protein proteolysis (GO:0033619)metalloendopeptidase activity (GO:0004222)metalloendopeptidase activity (GO:0004222)metalloendopeptidase activity (GO:0004222)metalloendopeptidase activity (GO:0004222)metallopeptidase activity (GO:0008237)metallopeptidase activity (GO:0008237)mitochondrial calcium ion homeostasis (GO:0051560)mitochondrial inner membrane (GO:0005743)mitochondrial inner membrane (GO:0005743)mitochondrial inner membrane (GO:0005743)mitochondrial inner membrane (GO:0005743)mitochondrial inner membrane (GO:0005743)mitochondrial inner membrane (GO:0005743)mitochondrial protein processing (GO:0034982)mitochondrial protein processing (GO:0034982)mitochondrial protein processing (GO:0034982)mitochondrial protein quality control (GO:0141164)mitochondrion (GO:0005739)mitochondrion (GO:0005739)mitochondrion (GO:0005739)protein autoprocessing (GO:0016540)protein autoprocessing (GO:0016540)protein binding (GO:0005515)protein catabolic process (GO:0030163)protein maturation (GO:0051604)protein maturation (GO:0051604)protein processing (GO:0016485)protein processing (GO:0016485)proteolysis (GO:0006508)proteolysis (GO:0006508)proteolysis (GO:0006508)regulation of calcium import into the mitochondrion (GO:0110097)regulation of calcium import into the mitochondrion (GO:0110097)unfolded protein binding (GO:0051082)zinc ion binding (GO:0008270)
Expression (TPM)
AFG3L2 — as a Regulated Gene

TFs regulating AFG3L2 0 TFs

Transcription factors with Perturb-seq knockdown data for AFG3L2. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = AFG3L2 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to AFG3L2

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of AFG3L2, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr18:12,253,776–12,254,799 122.9 kb Distal (>10kb) Multiome 162
chr18:12,271,329–12,272,193 105.4 kb Distal (>10kb) Multiome 601
chr18:12,287,265–12,288,653 89.7 kb Distal (>10kb) Multiome 353
chr18:12,288,796–12,289,337 88.2 kb Distal (>10kb) Multiome 159
chr18:12,307,278–12,309,118 69.0 kb Distal (>10kb) Multiome 646
chr18:12,376,065–12,378,406 239 bp At TSS Multiome 1012
chr18:12,407,513–12,408,521 30.7 kb Distal (>10kb) Multiome 637
chr18:12,419,774–12,420,625 42.9 kb Distal (>10kb) Multiome 579
chr18:12,420,869–12,421,324 43.9 kb Distal (>10kb) Multiome 417
chr18:12,657,070–12,658,817 280.9 kb Distal (>10kb) Multiome HiCAR 689

Genome Browser

Genomic view of the AFG3L2 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr18:12,243,776 – 12,668,817
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq