MBTPS1
membrane bound transcription factor peptidase, site 1 | KIAA0091, PCSK8, S1P, SKI-1

This gene encodes a member of the subtilisin-like proprotein convertase family, which includes proteases that process protein and peptide precursors trafficking through regulated or constitutive branches of the secretory pathway. The encoded protein undergoes an initial autocatalytic processing event in the ER to generate a heterodimer which exits the ER and sorts to the cis/medial-Golgi where a second autocatalytic event takes place and the catalytic activity is acquired. It encodes a type 1 membrane bound protease which is ubiquitously expressed and regulates cholesterol or lipid homeostasis via cleavage of substrates at non-basic residues. Mutations in this gene may be associated with lysosomal dysfunction. [provided by RefSeq, Feb 2014]

Member of: DE-2 DE-2.44
Biological processes 35 terms
Expression (TPM)
MBTPS1 — as a Regulated Gene

TFs regulating MBTPS1 0 TFs

Transcription factors with Perturb-seq knockdown data for MBTPS1. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = MBTPS1 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to MBTPS1

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of MBTPS1, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr16:83,840,075–83,841,171 276.4 kb Distal (>10kb) Multiome 136
chr16:83,888,352–83,889,387 228.0 kb Distal (>10kb) Multiome 237
chr16:83,898,559–83,899,828 217.8 kb Distal (>10kb) Multiome 773
chr16:83,926,399–83,927,376 190.0 kb Distal (>10kb) Multiome 532
chr16:83,968,110–83,968,725 148.4 kb Distal (>10kb) Multiome 261
chr16:84,013,600–84,015,009 102.6 kb Distal (>10kb) Multiome 388
chr16:84,043,411–84,043,885 73.1 kb Distal (>10kb) Multiome 292
chr16:84,062,518–84,063,095 53.9 kb Distal (>10kb) Multiome 330
chr16:84,116,331–84,117,716 67 bp At TSS Multiome 1013
chr16:84,144,637–84,145,742 28.4 kb Distal (>10kb) Multiome 679
chr16:84,186,615–84,187,246 70.2 kb Distal (>10kb) Multiome 848
chr16:84,268,108–84,268,844 151.6 kb Distal (>10kb) Multiome 42
chr16:84,367,919–84,368,944 251.6 kb Distal (>10kb) Multiome 287

Genome Browser

Genomic view of the MBTPS1 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr16:83,830,075 – 84,378,944
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq