IVD
isovaleryl-CoA dehydrogenase | ACAD2, IVDH

Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. Alternatively spliced transcript variants have been found for this gene. [provided by RefSeq, Aug 2017]

Member of: DE-5
Biological processes 25 terms
Expression (TPM)
IVD — as a Regulated Gene

TFs regulating IVD 0 TFs

Transcription factors with Perturb-seq knockdown data for IVD. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = IVD upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to IVD

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of IVD, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr15:40,108,639–40,109,491 296.8 kb Distal (>10kb) Multiome 798
chr15:40,160,791–40,161,326 244.8 kb Distal (>10kb) Multiome 762
chr15:40,323,099–40,324,127 82.3 kb Distal (>10kb) Multiome 737
chr15:40,357,707–40,358,772 47.6 kb Distal (>10kb) Multiome 515
chr15:40,367,875–40,368,398 37.6 kb Distal (>10kb) Multiome 846
chr15:40,405,523–40,406,103 66 bp At TSS Multiome 672
chr15:40,440,664–40,441,222 35.1 kb Distal (>10kb) Multiome 440
chr15:40,470,654–40,471,315 65.2 kb Distal (>10kb) Multiome 463
chr15:40,511,458–40,512,083 105.9 kb Distal (>10kb) Multiome 646
chr15:40,593,777–40,594,776 188.3 kb Distal (>10kb) Multiome 899
chr15:40,694,639–40,695,262 289.2 kb Distal (>10kb) Multiome 831

Genome Browser

Genomic view of the IVD locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr15:40,098,639 – 40,705,262
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq