GBA1
glucosylceramidase beta 1 | GBA, GLUC

This gene encodes a lysosomal membrane protein that cleaves the beta-glucosidic linkage of glycosylceramide, an intermediate in glycolipid metabolism. Mutations in this gene cause Gaucher disease, a lysosomal storage disease characterized by an accumulation of glucocerebrosides. A related pseudogene is approximately 12 kb downstream of this gene on chromosome 1. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2010]

Developmental clusters: GC6
Biological processes 77 terms
Golgi apparatus (GO:0005794)Golgi apparatus (GO:0005794)autophagy (GO:0006914)autophagy (GO:0006914)beta-glucosidase activity (GO:0008422)beta-glucosidase activity (GO:0008422)beta-glucosidase activity (GO:0008422)beta-glucoside catabolic process (GO:1901805)cellular response to starvation (GO:0009267)cellular response to tumor necrosis factor (GO:0071356)ceramide biosynthetic process (GO:0046513)cholesterol metabolic process (GO:0008203)cholesterol metabolic process (GO:0008203)endoplasmic reticulum (GO:0005783)endoplasmic reticulum (GO:0005783)establishment of skin barrier (GO:0061436)extracellular exosome (GO:0070062)extracellular region (GO:0005576)galactosylceramidase activity (GO:0004336)glucosylceramidase activity (GO:0004348)glucosylceramidase activity (GO:0004348)glucosylceramidase activity (GO:0004348)glucosylceramidase activity (GO:0004348)glucosylceramide catabolic process (GO:0006680)glucosylceramide catabolic process (GO:0006680)glucosylceramide catabolic process (GO:0006680)glucosylceramide catabolic process (GO:0006680)glucosyltransferase activity (GO:0046527)glucosyltransferase activity (GO:0046527)glycolipid biosynthetic process (GO:0009247)glycolipid biosynthetic process (GO:0009247)glycolipid catabolic process (GO:0019377)hydrolase activity (GO:0016787)lysosomal lumen (GO:0043202)lysosomal lumen (GO:0043202)lysosomal membrane (GO:0005765)lysosomal membrane (GO:0005765)lysosomal membrane (GO:0005765)lysosomal membrane (GO:0005765)lysosomal membrane (GO:0005765)lysosomal membrane (GO:0005765)lysosomal protein catabolic process (GO:1905146)lysosome (GO:0005764)lysosome (GO:0005764)lysosome organization (GO:0007040)lysosome organization (GO:0007040)mitochondrion organization (GO:0007005)negative regulation of MAPK cascade (GO:0043409)negative regulation of inflammatory response (GO:0050728)negative regulation of interleukin-6 production (GO:0032715)neuron projection development (GO:0031175)positive regulation of neuronal action potential (GO:1904457)protein binding (GO:0005515)protein catabolic process (GO:0030163)regulation of TOR signaling (GO:0032006)regulation of TOR signaling (GO:0032006)regulation of lysosomal protein catabolic process (GO:1905165)regulation of macroautophagy (GO:0016241)regulation of macroautophagy (GO:0016241)regulation of membrane potential (GO:0042391)regulation of protein catabolic process (GO:0042176)response to dexamethasone (GO:0071548)response to estrogen (GO:0043627)response to pH (GO:0009268)response to testosterone (GO:0033574)response to thyroid hormone (GO:0097066)scavenger receptor binding (GO:0005124)signaling receptor binding (GO:0005102)signaling receptor binding (GO:0005102)skin epidermis development (GO:0098773)sphingolipid metabolic process (GO:0006665)sphingosine biosynthetic process (GO:0046512)steryl-beta-glucosidase activity (GO:0050295)steryl-beta-glucosidase activity (GO:0050295)termination of signal transduction (GO:0023021)trans-Golgi network (GO:0005802)trans-Golgi network (GO:0005802)
Expression (TPM)
GBA1 — as a Regulated Gene

TFs regulating GBA1 0 TFs

Transcription factors with Perturb-seq knockdown data for GBA1. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = GBA1 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to GBA1

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of GBA1, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr1:155,241,181–155,241,363 at TSS At TSS 299
chr1:155,244,103–155,245,349 2.9 kb Proximal (<10kb) 900
chr1:155,250,356–155,251,199 9.1 kb Proximal (<10kb) 605

Genome Browser

Genomic view of the GBA1 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr1:155,231,181 – 155,261,199
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq