CTNS
cystinosin, lysosomal cystine transporter | CTNS-LSB, PQLC4, SLC66A4

This gene encodes a seven-transmembrane domain protein that functions to transport cystine out of lysosomes. Its activity is driven by the H+ electrochemical gradient of the lysosomal membrane. Mutations in this gene cause cystinosis, a lysosomal storage disorder. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jul 2009]

Biological processes 43 terms
ATP metabolic process (GO:0046034)L-cystine transmembrane transporter activity (GO:0015184)L-cystine transmembrane transporter activity (GO:0015184)L-cystine transmembrane transporter activity (GO:0015184)L-cystine transmembrane transporter activity (GO:0015184)L-cystine transmembrane transporter activity (GO:0015184)L-cystine transmembrane transporter activity (GO:0015184)L-cystine transport (GO:0015811)L-cystine transport (GO:0015811)L-cystine transport (GO:0015811)L-cystine transport (GO:0015811)L-cystine transport (GO:0015811)amino acid metabolic process (GO:0006520)animal organ development (GO:0048513)brain development (GO:0007420)cognition (GO:0050890)cognition (GO:0050890)early endosome (GO:0005769)extracellular exosome (GO:0070062)glutathione metabolic process (GO:0006749)late endosome (GO:0005770)lysosomal membrane (GO:0005765)lysosomal membrane (GO:0005765)lysosomal membrane (GO:0005765)lysosomal membrane (GO:0005765)lysosomal membrane (GO:0005765)lysosomal membrane (GO:0005765)lysosome (GO:0005764)lysosome (GO:0005764)melanosome (GO:0042470)melanosome membrane (GO:0033162)oligopeptide transmembrane transport (GO:0035672)plasma membrane (GO:0005886)plasma membrane (GO:0005886)positive regulation of TORC1 signaling (GO:1904263)protein binding (GO:0005515)proton transmembrane transport (GO:1902600)regulation of TORC1 signaling (GO:1903432)regulation of TORC1 signaling (GO:1903432)regulation of melanin biosynthetic process (GO:0048021)solute:proton symporter activity (GO:0015295)system development (GO:0048731)transmembrane transport (GO:0055085)
Expression (TPM)
CTNS — as a Regulated Gene

TFs regulating CTNS 0 TFs

Transcription factors with Perturb-seq knockdown data for CTNS. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = CTNS upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to CTNS

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of CTNS, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr17:3,529,956–3,530,848 106.0 kb Distal (>10kb) Multiome 320
chr17:3,535,341–3,536,205 100.8 kb Distal (>10kb) Multiome 356
chr17:3,546,350–3,546,812 89.8 kb Distal (>10kb) Multiome 106
chr17:3,635,650–3,637,225 21 bp At TSS Multiome 866
chr17:3,667,393–3,669,475 32.2 kb Distal (>10kb) Multiome 949
chr17:3,723,432–3,724,429 87.4 kb Distal (>10kb) Multiome 865
chr17:3,754,197–3,755,835 118.4 kb Distal (>10kb) Multiome 396
chr17:3,845,518–3,846,549 209.8 kb Distal (>10kb) Multiome 917
chr17:3,891,925–3,893,745 256.8 kb Distal (>10kb) Multiome 716

Genome Browser

Genomic view of the CTNS locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr17:3,519,956 – 3,903,745
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq