CLN3
CLN3 lysosomal/endosomal transmembrane protein, battenin | BTN1, JNCL, SLC29B1, BTS

This gene encodes a protein that is involved in lysosomal function. Mutations in this, as well as other neuronal ceroid-lipofuscinosis (CLN) genes, cause neurodegenerative diseases commonly known as Batten disease or collectively known as neuronal ceroid lipofuscinoses (NCLs). Many alternatively spliced transcript variants have been found for this gene. [provided by RefSeq, Jul 2008]

Member of: DE-1
Biological processes 140 terms
Golgi apparatus (GO:0005794)Golgi apparatus (GO:0005794)Golgi apparatus (GO:0005794)Golgi apparatus (GO:0005794)Golgi membrane (GO:0000139)Golgi membrane (GO:0000139)Golgi membrane (GO:0000139)Golgi stack (GO:0005795)Golgi stack (GO:0005795)Golgi to lysosome transport (GO:0090160)Golgi to lysosome transport (GO:0090160)L-arginine transmembrane transport (GO:1903826)action potential (GO:0001508)amino acid transport (GO:0006865)amino acid transport (GO:0006865)amyloid precursor protein catabolic process (GO:0042987)associative learning (GO:0008306)autolysosome (GO:0044754)autolysosome (GO:0044754)autophagosome (GO:0005776)autophagosome (GO:0005776)autophagosome maturation (GO:0097352)autophagosome-lysosome fusion (GO:0061909)autophagosome-lysosome fusion (GO:0061909)calcium-dependent protein binding (GO:0048306)caveola (GO:0005901)caveola (GO:0005901)caveola (GO:0005901)ceramide transport (GO:0035627)cytoplasm (GO:0005737)cytoplasmic vesicle (GO:0031410)cytosol (GO:0005829)early endosome (GO:0005769)early endosome (GO:0005769)early endosome membrane (GO:0031901)early endosome membrane (GO:0031901)endocytosis (GO:0006897)endoplasmic reticulum (GO:0005783)endoplasmic reticulum membrane (GO:0005789)glycerophospholipid biosynthetic process (GO:0046474)glycolipid binding (GO:0051861)glycolipid transfer activity (GO:0017089)glycolipid transport (GO:0046836)intracellular monoatomic cation homeostasis (GO:0030003)intracellular water homeostasis (GO:0009992)intracellular water homeostasis (GO:0009992)ionotropic glutamate receptor signaling pathway (GO:0035235)late endosome (GO:0005770)late endosome (GO:0005770)late endosome (GO:0005770)late endosome (GO:0005770)late endosome (GO:0005770)late endosome membrane (GO:0031902)learning or memory (GO:0007611)learning or memory (GO:0007611)lysosomal lumen acidification (GO:0007042)lysosomal lumen pH elevation (GO:0035752)lysosomal lumen pH elevation (GO:0035752)lysosomal membrane (GO:0005765)lysosomal membrane (GO:0005765)lysosomal membrane (GO:0005765)lysosomal membrane (GO:0005765)lysosomal protein catabolic process (GO:1905146)lysosomal protein catabolic process (GO:1905146)lysosome (GO:0005764)lysosome (GO:0005764)lysosome (GO:0005764)lysosome (GO:0005764)lysosome organization (GO:0007040)lysosome organization (GO:0007040)membrane (GO:0016020)membrane (GO:0016020)membrane organization (GO:0061024)membrane organization (GO:0061024)membrane raft (GO:0045121)membrane raft (GO:0045121)membrane raft (GO:0045121)negative regulation of apoptotic process (GO:0043066)negative regulation of apoptotic process (GO:0043066)negative regulation of apoptotic process (GO:0043066)negative regulation of neuron apoptotic process (GO:0043524)negative regulation of proteolysis (GO:0045861)neuromuscular process controlling balance (GO:0050885)neuron projection (GO:0043005)neuron projection (GO:0043005)nucleus (GO:0005634)phagosome-lysosome docking (GO:0090384)phagosome-lysosome docking (GO:0090384)phagosome-lysosome fusion (GO:0090385)phagosome-lysosome fusion (GO:0090385)plasma membrane (GO:0005886)plasma membrane (GO:0005886)plasma membrane (GO:0005886)plasma membrane raft organization (GO:0044857)plasma membrane raft organization (GO:0044857)positive regulation of Golgi to plasma membrane protein transport (GO:0042998)positive regulation of Golgi to plasma membrane protein transport (GO:0042998)positive regulation of caveolin-mediated endocytosis (GO:2001288)positive regulation of caveolin-mediated endocytosis (GO:2001288)positive regulation of pinocytosis (GO:0048549)positive regulation of pinocytosis (GO:0048549)protein binding (GO:0005515)protein processing (GO:0016485)receptor-mediated endocytosis (GO:0006898)receptor-mediated endocytosis (GO:0006898)recycling endosome (GO:0055037)recycling endosome (GO:0055037)regulation of arginine biosynthetic process (GO:1900079)regulation of arginine biosynthetic process (GO:1900079)regulation of autophagosome maturation (GO:1901096)regulation of autophagosome maturation (GO:1901096)regulation of autophagosome size (GO:0016243)regulation of autophagy (GO:0010506)regulation of cellular response to osmotic stress (GO:0106049)regulation of cytoskeleton organization (GO:0051493)regulation of cytosolic calcium ion concentration (GO:0051480)regulation of fibroblast migration (GO:0010762)regulation of modification of synaptic structure (GO:1905244)regulation of modification of synaptic structure (GO:1905244)regulation of phagosome maturation (GO:1905162)regulation of phagosome maturation (GO:1905162)regulation of protein localization to plasma membrane (GO:1903076)regulation of protein localization to plasma membrane (GO:1903076)regulation of protein processing (GO:0070613)regulation of proteolysis (GO:0030162)regulation of short-term neuronal synaptic plasticity (GO:0048172)regulation of short-term neuronal synaptic plasticity (GO:0048172)regulation of synaptic transmission, GABAergic (GO:0032228)regulation of synaptic transmission, GABAergic (GO:0032228)regulation of synaptic transmission, glutamatergic (GO:0051966)regulation of synaptic transmission, glutamatergic (GO:0051966)renal potassium excretion (GO:0036359)renal potassium excretion (GO:0036359)sulfatide binding (GO:0120146)synapse (GO:0045202)synaptic vesicle (GO:0008021)trans-Golgi network (GO:0005802)trans-Golgi network (GO:0005802)vesicle transport along microtubule (GO:0047496)vesicle transport along microtubule (GO:0047496)
Expression (TPM)
CLN3 — as a Regulated Gene

TFs regulating CLN3 0 TFs

Transcription factors with Perturb-seq knockdown data for CLN3. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = CLN3 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to CLN3

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of CLN3, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr16:28,211,165–28,212,644 279.9 kb Distal (>10kb) Multiome 960
chr16:28,267,361–28,267,924 224.4 kb Distal (>10kb) Multiome 36
chr16:28,277,564–28,278,417 214.1 kb Distal (>10kb) Multiome 598
chr16:28,291,632–28,293,697 198.5 kb Distal (>10kb) Multiome 578
chr16:28,491,428–28,492,451 74 bp At TSS Multiome 879
chr16:28,553,780–28,554,756 62.2 kb Distal (>10kb) Multiome 995

Genome Browser

Genomic view of the CLN3 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr16:28,201,165 – 28,564,756
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq