ADAMTS13
ADAM metallopeptidase with thrombospondin type 1 motif 13 | DKFZp434C2322, FLJ42993, MGC118899, MGC118900, TTP, VWFCP, vWF-CP, C9orf8

This gene encodes a member of a family of proteins containing several distinct regions, including a metalloproteinase domain, a disintegrin-like domain, and a thrombospondin type 1 (TS) motif. The enzyme encoded by this gene specifically cleaves von Willebrand Factor (vWF). Defects in this gene are associated with thrombotic thrombocytopenic purpura. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jul 2013]

Developmental clusters: GC6
Biological processes 41 terms
blood coagulation (GO:0007596)calcium ion binding (GO:0005509)cell surface (GO:0009986)cell-matrix adhesion (GO:0007160)cellular response to interleukin-4 (GO:0071353)cellular response to lipopolysaccharide (GO:0071222)cellular response to tumor necrosis factor (GO:0071356)cellular response to type II interferon (GO:0071346)endopeptidase activity (GO:0004175)endoplasmic reticulum lumen (GO:0005788)extracellular matrix (GO:0031012)extracellular matrix (GO:0031012)extracellular matrix organization (GO:0030198)extracellular matrix organization (GO:0030198)extracellular region (GO:0005576)extracellular region (GO:0005576)glycoprotein metabolic process (GO:0009100)integrin binding (GO:0005178)integrin-mediated signaling pathway (GO:0007229)metalloendopeptidase activity (GO:0004222)metalloendopeptidase activity (GO:0004222)metalloendopeptidase activity (GO:0004222)metalloendopeptidase activity (GO:0004222)metallopeptidase activity (GO:0008237)metallopeptidase activity (GO:0008237)peptidase activity (GO:0008233)peptide catabolic process (GO:0043171)platelet activation (GO:0030168)protein binding (GO:0005515)protein catabolic process (GO:0030163)protein processing (GO:0016485)proteolysis (GO:0006508)proteolysis (GO:0006508)proteolysis (GO:0006508)response to amine (GO:0014075)response to interleukin-4 (GO:0070670)response to potassium ion (GO:0035864)response to toxic substance (GO:0009636)response to tumor necrosis factor (GO:0034612)response to type II interferon (GO:0034341)zinc ion binding (GO:0008270)
Expression (TPM)
ADAMTS13 — as a Regulated Gene

TFs regulating ADAMTS13 0 TFs

Transcription factors with Perturb-seq knockdown data for ADAMTS13. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = ADAMTS13 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to ADAMTS13

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of ADAMTS13, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr9:133,144,161–133,144,920 277.4 kb Distal (>10kb) Multiome 776
chr9:133,147,412–133,149,938 272.6 kb Distal (>10kb) Multiome 979
chr9:133,163,575–133,164,128 258.1 kb Distal (>10kb) Multiome 308
chr9:133,238,117–133,239,420 183.3 kb Distal (>10kb) Multiome 620
chr9:133,335,737–133,336,702 85.8 kb Distal (>10kb) Multiome 1038
chr9:133,347,434–133,348,830 73.8 kb Distal (>10kb) Multiome 893
chr9:133,356,029–133,357,223 65.4 kb Distal (>10kb) Multiome 648
chr9:133,375,394–133,376,740 45.8 kb Distal (>10kb) Multiome 834
chr9:133,417,747–133,418,516 3.9 kb Proximal (<10kb) Multiome 1015
chr9:133,428,444–133,429,113 6.7 kb Proximal (<10kb) Multiome 255
chr9:133,429,621–133,430,196 7.9 kb Proximal (<10kb) Multiome 197
chr9:133,458,883–133,460,984 37.9 kb Distal (>10kb) Multiome 835
chr9:133,478,485–133,479,696 57.2 kb Distal (>10kb) Multiome 653
chr9:133,534,455–133,535,168 112.7 kb Distal (>10kb) Multiome 295
chr9:133,608,924–133,609,730 187.4 kb Distal (>10kb) Multiome 411
chr9:133,738,059–133,738,688 316.3 kb Distal (>10kb) Multiome 451

Genome Browser

Genomic view of the ADAMTS13 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr9:133,134,161 – 133,748,688
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq