USH1C
USH1 protein network component harmonin | AIE-75, NY-CO-37, NY-CO-38, PDZ-73, PDZ73, PDZD7C, harmonin, DFNB18

This gene encodes a scaffold protein that functions in the assembly of Usher protein complexes. The protein contains PDZ domains, a coiled-coil region with a bipartite nuclear localization signal and a PEST degradation sequence. Defects in this gene are the cause of Usher syndrome type 1C and non-syndromic sensorineural deafness autosomal recessive type 18. Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Mar 2009]

Biological processes 47 terms
G2/M transition of mitotic cell cycle (GO:0000086)actin filament bundle assembly (GO:0051017)apical part of cell (GO:0045177)auditory receptor cell morphogenesis (GO:0002093)brush border (GO:0005903)brush border (GO:0005903)brush border assembly (GO:1904970)brush border assembly (GO:1904970)brush border assembly (GO:1904970)brush border assembly (GO:1904970)cilium (GO:0005929)cytoplasm (GO:0005737)cytoskeleton (GO:0005856)cytosol (GO:0005829)cytosol (GO:0005829)equilibrioception (GO:0050957)inner ear auditory receptor cell differentiation (GO:0042491)inner ear morphogenesis (GO:0042472)inner ear receptor cell stereocilium organization (GO:0060122)inner ear receptor cell stereocilium organization (GO:0060122)microvillus (GO:0005902)microvillus (GO:0005902)neuromuscular process controlling balance (GO:0050885)parallel actin filament bundle assembly (GO:0030046)photoreceptor cell maintenance (GO:0045494)photoreceptor inner segment (GO:0001917)photoreceptor inner segment (GO:0001917)photoreceptor outer segment (GO:0001750)plasma membrane (GO:0005886)plasma membrane (GO:0005886)protein binding (GO:0005515)protein localization to microvillus (GO:1904106)protein localization to microvillus (GO:1904106)protein localization to microvillus (GO:1904106)protein-containing complex assembly (GO:0065003)regulation of microvillus length (GO:0032532)retinal cone cell development (GO:0046549)sensory perception of light stimulus (GO:0050953)sensory perception of sound (GO:0007605)sensory perception of sound (GO:0007605)sensory perception of sound (GO:0007605)spectrin binding (GO:0030507)stereocilia ankle link complex (GO:0002142)stereocilium (GO:0032420)stereocilium (GO:0032420)stereocilium tip (GO:0032426)synapse (GO:0045202)
Expression (TPM)
USH1C — as a Regulated Gene

TFs regulating USH1C 0 TFs

Transcription factors with Perturb-seq knockdown data for USH1C. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = USH1C upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to USH1C

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of USH1C, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr11:17,543,883–17,544,680 at TSS At TSS 193
chr11:17,546,803–17,547,775 2.4 kb Proximal (<10kb) 187
chr11:17,548,543–17,548,745 4.1 kb Proximal (<10kb) 27

Genome Browser

Genomic view of the USH1C locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr11:17,533,883 – 17,558,745
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq