TAFAZZIN
tafazzin, phospholipid-lysophospholipid transacylase | BTHS, G4.5, TAZ1, CMD3A, EFE, EFE2, TAZ

This gene encodes a protein that is expressed at high levels in cardiac and skeletal muscle. Mutations in this gene have been associated with a number of clinical disorders including Barth syndrome, dilated cardiomyopathy (DCM), hypertrophic DCM, endocardial fibroelastosis, and left ventricular noncompaction (LVNC). Multiple transcript variants encoding different isoforms have been described. A long form and a short form of each of these isoforms is produced; the short form lacks a hydrophobic leader sequence and may exist as a cytoplasmic protein rather than being membrane-bound. Other alternatively spliced transcripts have been described but the full-length nature of all these transcripts is not known. [provided by RefSeq, Jul 2008]

Member of: DE-6
Biological processes 26 terms
Expression (TPM)
TAFAZZIN — as a Regulated Gene

TFs regulating TAFAZZIN 0 TFs

Transcription factors with Perturb-seq knockdown data for TAFAZZIN. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = TAFAZZIN upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to TAFAZZIN

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of TAFAZZIN, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chrX:154,136,648–154,137,146 275.3 kb Distal (>10kb) Multiome 391
chrX:154,368,993–154,370,053 42.6 kb Distal (>10kb) Multiome 546
chrX:154,370,757–154,372,188 40.8 kb Distal (>10kb) Multiome 764
chrX:154,378,063–154,379,701 33.2 kb Distal (>10kb) Multiome 687
chrX:154,397,430–154,398,941 13.9 kb Distal (>10kb) Multiome 871
chrX:154,409,052–154,409,671 2.8 kb Proximal (<10kb) Multiome 396
chrX:154,411,411–154,411,578 at TSS At TSS 498
chrX:154,412,051–154,412,257 528 bp At TSS 312
chrX:154,428,419–154,428,969 16.5 kb Distal (>10kb) Multiome 601
chrX:154,436,501–154,437,435 24.8 kb Distal (>10kb) Multiome 448
chrX:154,443,986–154,444,454 32.0 kb Distal (>10kb) Multiome 329
chrX:154,457,605–154,458,763 45.9 kb Distal (>10kb) Multiome 467
chrX:154,478,385–154,479,590 66.9 kb Distal (>10kb) Multiome 707
chrX:154,486,385–154,487,035 74.6 kb Distal (>10kb) Multiome 437
chrX:154,490,259–154,491,245 78.6 kb Distal (>10kb) Multiome 567
chrX:154,515,811–154,517,059 104.2 kb Distal (>10kb) Multiome 590
chrX:154,546,514–154,547,906 135.1 kb Distal (>10kb) Multiome 691

Genome Browser

Genomic view of the TAFAZZIN locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chrX:154,126,648 – 154,557,906
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq