RHBDD1
rhomboid domain containing 1 | DKFZp547E052, RHBDL4

Enables serine-type endopeptidase activity. Involved in several processes, including cellular response to unfolded protein; membrane protein proteolysis; and positive regulation of protein catabolic process. Located in endoplasmic reticulum. [provided by Alliance of Genome Resources, Jul 2025]

Member of: DE-3 DE-3.26
Biological processes 45 terms
ERAD pathway (GO:0036503)ERAD pathway (GO:0036503)cellular response to UV (GO:0034644)cellular response to UV (GO:0034644)cellular response to unfolded protein (GO:0034620)cellular response to unfolded protein (GO:0034620)cellular response to unfolded protein (GO:0034620)cellular response to unfolded protein (GO:0034620)endopeptidase activity (GO:0004175)endoplasmic reticulum (GO:0005783)endoplasmic reticulum (GO:0005783)endoplasmic reticulum (GO:0005783)endoplasmic reticulum membrane (GO:0005789)endoplasmic reticulum membrane (GO:0005789)endoplasmic reticulum quality control compartment (GO:0044322)endoplasmic reticulum quality control compartment (GO:0044322)membrane (GO:0016020)membrane protein intracellular domain proteolysis (GO:0031293)membrane protein intracellular domain proteolysis (GO:0031293)membrane protein proteolysis (GO:0033619)membrane protein proteolysis (GO:0033619)membrane protein proteolysis (GO:0033619)mitochondrial membrane (GO:0031966)negative regulation of apoptotic process (GO:0043066)negative regulation of apoptotic process (GO:0043066)negative regulation of apoptotic process (GO:0043066)negative regulation of apoptotic process (GO:0043066)negative regulation of apoptotic process (GO:0043066)peptidase activity (GO:0008233)positive regulation of protein catabolic process (GO:0045732)positive regulation of protein catabolic process (GO:0045732)positive regulation of protein metabolic process (GO:0051247)positive regulation of protein processing (GO:0010954)positive regulation of protein processing (GO:0010954)positive regulation of secretion (GO:0051047)post-translational protein modification (GO:0043687)post-translational protein modification (GO:0043687)protein binding (GO:0005515)regulation of male germ cell proliferation (GO:2000254)retrograde protein transport, ER to cytosol (GO:0030970)serine-type endopeptidase activity (GO:0004252)serine-type endopeptidase activity (GO:0004252)serine-type endopeptidase activity (GO:0004252)spermatid differentiation (GO:0048515)spermatid differentiation (GO:0048515)
Expression (TPM)
RHBDD1 — as a Regulated Gene

TFs regulating RHBDD1 0 TFs

Transcription factors with Perturb-seq knockdown data for RHBDD1. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = RHBDD1 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to RHBDD1

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of RHBDD1, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr2:226,649,671–226,650,681 185.7 kb Distal (>10kb) Multiome 758
chr2:226,720,273–226,721,822 115.0 kb Distal (>10kb) Multiome 136
chr2:226,790,932–226,792,958 44.3 kb Distal (>10kb) Multiome 707
chr2:226,797,838–226,801,976 34.8 kb Distal (>10kb) Multiome 1020
chr2:226,835,365–226,836,725 47 bp At TSS Multiome 964
chr2:226,874,251–226,875,681 38.8 kb Distal (>10kb) Multiome 292

Genome Browser

Genomic view of the RHBDD1 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr2:226,639,671 – 226,885,681
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq