HSD17B10
hydroxysteroid 17-beta dehydrogenase 10 | 17b-HSD10, ABAD, CAMR, ERAB, MHBD, MRPP2, SDR5C1, HADH2, MRXS10

This gene encodes 3-hydroxyacyl-CoA dehydrogenase type II, a member of the short-chain dehydrogenase/reductase superfamily. The gene product is a mitochondrial protein that catalyzes the oxidation of a wide variety of fatty acids and steroids, and is a subunit of mitochondrial ribonuclease P, which is involved in tRNA maturation. The protein has been implicated in the development of Alzheimer disease, and mutations in the gene are the cause of 17beta-hydroxysteroid dehydrogenase type 10 (HSD10) deficiency. Several alternatively spliced transcript variants have been identified, but the full-length nature of only two transcript variants has been determined. [provided by RefSeq, Aug 2014]

Member of: DE-1 DE-1.47
Biological processes 57 terms
(3S)-3-hydroxyacyl-CoA dehydrogenase (NAD+) activity (GO:0003857)(3S)-3-hydroxyacyl-CoA dehydrogenase (NAD+) activity (GO:0003857)17-beta-hydroxysteroid dehydrogenase (NAD+) activity (GO:0044594)3-hydroxy-2-methylbutyryl-CoA dehydrogenase activity (GO:0047015)3-hydroxy-2-methylbutyryl-CoA dehydrogenase activity (GO:0047015)C21-steroid hormone metabolic process (GO:0008207)L-isoleucine catabolic process (GO:0006550)L-isoleucine catabolic process (GO:0006550)RNA binding (GO:0003723)androgen metabolic process (GO:0008209)androgen metabolic process (GO:0008209)androstan-3-alpha,17-beta-diol dehydrogenase (NAD+) activity (GO:0047044)bile acid biosynthetic process (GO:0006699)bile acid biosynthetic process (GO:0006699)brexanolone metabolic process (GO:0062173)cardiolipin dehydrogenase (NAD+) activity (GO:0160241)chenodeoxycholate 7-alpha-dehydrogenase (NAD+) activity (GO:0106281)chenodeoxycholate 7-alpha-dehydrogenase (NAD+) activity (GO:0106281)cholate 7-alpha-dehydrogenase (NAD+) activity (GO:0008709)cholate 7-alpha-dehydrogenase (NAD+) activity (GO:0008709)cholate 7-alpha-dehydrogenase (NAD+) activity (GO:0008709)cytoplasm (GO:0005737)estradiol 17-beta-dehydrogenase [NAD(P)+] activity (GO:0004303)estradiol 17-beta-dehydrogenase [NAD(P)+] activity (GO:0004303)estrogen metabolic process (GO:0008210)estrogen metabolic process (GO:0008210)fatty acid beta-oxidation (GO:0006635)fatty acid beta-oxidation (GO:0006635)fatty acid metabolic process (GO:0006631)isoursodeoxycholate 7-beta-dehydrogenase (NAD+) activity (GO:0106282)isoursodeoxycholate 7-beta-dehydrogenase (NAD+) activity (GO:0106282)lipid metabolic process (GO:0006629)mitochondrial matrix (GO:0005759)mitochondrial nucleoid (GO:0042645)mitochondrial nucleoid (GO:0042645)mitochondrial ribonuclease P complex (GO:0030678)mitochondrial ribonuclease P complex (GO:0030678)mitochondrial tRNA 3'-end processing (GO:1990180)mitochondrial tRNA 5'-end processing (GO:0097745)mitochondrial tRNA methylation (GO:0070901)mitochondrion (GO:0005739)mitochondrion (GO:0005739)mitochondrion (GO:0005739)mitochondrion (GO:0005739)mitochondrion (GO:0005739)mitochondrion (GO:0005739)mitochondrion organization (GO:0007005)plasma membrane (GO:0005886)protein binding (GO:0005515)protein homotetramerization (GO:0051289)tRNA 3'-end processing (GO:0042780)tRNA 3'-terminal CCA addition (GO:0001680)tRNA binding (GO:0000049)testosterone dehydrogenase (NAD+) activity (GO:0047035)testosterone dehydrogenase (NAD+) activity (GO:0047035)ursodeoxycholate 7-beta-dehydrogenase (NAD+) activity (GO:0106283)ursodeoxycholate 7-beta-dehydrogenase (NAD+) activity (GO:0106283)
Expression (TPM)
HSD17B10 — as a Regulated Gene

TFs regulating HSD17B10 0 TFs

Transcription factors with Perturb-seq knockdown data for HSD17B10. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = HSD17B10 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to HSD17B10

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of HSD17B10, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chrX:53,224,805–53,225,756 209.0 kb Distal (>10kb) Multiome 825
chrX:53,421,898–53,423,292 11.6 kb Distal (>10kb) Multiome 745
chrX:53,434,290–53,434,606 at TSS At TSS 423
chrX:53,441,598–53,442,101 7.5 kb Proximal (<10kb) Multiome 254
chrX:53,683,043–53,684,640 249.9 kb Distal (>10kb) Multiome 710
chrX:53,686,122–53,687,094 252.3 kb Distal (>10kb) Multiome 540

Genome Browser

Genomic view of the HSD17B10 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chrX:53,214,805 – 53,697,094
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq