ABCC8
ATP binding cassette subfamily C member 8 | ABC36, HHF1, HI, MRP8, PHHI, SUR1, TNDM2, HRINS, SUR

The protein encoded by this gene is a member of the superfamily of ATP-binding cassette (ABC) transporters. ABC proteins transport various molecules across extra- and intra-cellular membranes. ABC genes are divided into seven distinct subfamilies (ABC1, MDR/TAP, MRP, ALD, OABP, GCN20, White). This protein is a member of the MRP subfamily which is involved in multi-drug resistance. This protein functions as a modulator of ATP-sensitive potassium channels and insulin release. Mutations in the ABCC8 gene and deficiencies in the encoded protein have been observed in patients with hyperinsulinemic hypoglycemia of infancy, an autosomal recessive disorder of unregulated and high insulin secretion. Mutations have also been associated with non-insulin-dependent diabetes mellitus type II, an autosomal dominant disease of defective insulin secretion. Alternatively spliced transcript variants have been found for this gene. [provided by RefSeq, Jul 2020]

Biological processes 54 terms
ABC-type transporter activity (GO:0140359)ABC-type transporter activity (GO:0140359)ADP binding (GO:0043531)ATP binding (GO:0005524)ATP binding (GO:0005524)ATP hydrolysis activity (GO:0016887)ATP-activated inward rectifier potassium channel activity (GO:0015272)ATP-activated inward rectifier potassium channel activity (GO:0015272)ATPase-coupled monoatomic cation transmembrane transporter activity (GO:0019829)ATPase-coupled monoatomic cation transmembrane transporter activity (GO:0019829)female pregnancy (GO:0007565)intracellular glucose homeostasis (GO:0001678)inward rectifying potassium channel (GO:0008282)inward rectifying potassium channel (GO:0008282)membrane (GO:0016020)memory (GO:0007613)negative regulation of angiogenesis (GO:0016525)negative regulation of blood-brain barrier permeability (GO:1905604)negative regulation of glial cell proliferation (GO:0060253)negative regulation of insulin secretion (GO:0046676)negative regulation of low-density lipoprotein particle clearance (GO:0010989)negative regulation of neuroblast migration (GO:0061855)negative regulation of neurogenesis (GO:0050768)plasma membrane (GO:0005886)plasma membrane (GO:0005886)plasma membrane (GO:0005886)positive regulation of insulin secretion involved in cellular response to glucose stimulus (GO:0035774)positive regulation of potassium ion transport (GO:0043268)positive regulation of tight junction disassembly (GO:1905075)positive regulation of tumor necrosis factor production (GO:0032760)positive regulation of uterine smooth muscle relaxation (GO:1900721)potassium channel activity (GO:0005267)potassium ion import across plasma membrane (GO:1990573)potassium ion transmembrane transport (GO:0071805)potassium ion transport (GO:0006813)potassium ion transport (GO:0006813)potassium ion-transporting ATPase complex (GO:0031004)presynaptic membrane (GO:0042734)protein binding (GO:0005515)regulation of insulin secretion (GO:0050796)regulation of insulin secretion (GO:0050796)response to insulin (GO:0032868)response to lipopolysaccharide (GO:0032496)response to pH (GO:0009268)response to xenobiotic stimulus (GO:0009410)response to zinc ion (GO:0010043)sarcolemma (GO:0042383)sulfonylurea receptor activity (GO:0008281)synaptic vesicle membrane (GO:0030672)transmembrane transport (GO:0055085)transmembrane transport (GO:0055085)transmembrane transport (GO:0055085)transmembrane transporter binding (GO:0044325)visual learning (GO:0008542)
Expression (TPM)
ABCC8 — as a Regulated Gene

TFs regulating ABCC8 0 TFs

Transcription factors with Perturb-seq knockdown data for ABCC8. The Binding column indicates whether any binding evidence exists for this TF–gene pair (ChIP-seq or motif footprint peaks). The Mean coef is the average Perturb-seq regression coefficient across active gRNAs (positive = ABCC8 upregulated upon KD; negative = downregulated). The Outlier column indicates whether this gene is in the top or bottom 5% of all TF knockdown effects.

Data: Effect:
TF Mean coef Binding Outlier TF→Gene link

Elements linked to ABCC8

Open chromatin peaks (ATAC-seq) in the genomic neighbourhood of ABCC8, linked by TSS proximity or chromatin conformation (Multiome / HiCAR). Each element overlaps at least one TF ChIP-seq binding site — the TFs column shows how many distinct TFs bind that element.

Accessibility Element Dist. to TSS Link type TFs
chr11:17,473,408–17,473,691 3.0 kb Proximal (<10kb) 131
chr11:17,476,035–17,477,288 at TSS At TSS 247
chr11:17,479,602–17,479,843 2.9 kb Proximal (<10kb) 175

Genome Browser

Genomic view of the ABCC8 locus showing ATAC-seq accessibility and RNA-seq expression across the ESC → DE time course, together with TF binding peaks and element-to-TSS loop connections.

chr11:17,463,408 – 17,489,843
Proximal 1 kb Distal 10 kb Multiome HiCAR ATAC-seq RNA-seq